Nur 311 Exam 2 with precise detailed solutions

Nur 311 Exam 2 with precise !| !| !| !| !| !|




detailed solutions !|




PKU diet to follow - Correct answer ✔Breast Feeding or PA+ Free Formula.
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Restricted PA + Intake Throughout Life; No meat, limited fruits &
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vegetables, limited grains !| !|




What happens if people with PKU don't follow their diet - Correct answer
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✔Short Attention Span !| !|




Poor short term memory
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Visual perception problems
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Poor motor coordination
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Mood disorders !|




Brain structural changes (reduced grey matter)
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Safe PKU level - Correct answer ✔2-6mg/dl
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PKU nursing Considerations - Correct answer ✔Assist with testing
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Teach parents about diet and need for follow up blood levels throughout life
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Child may have trouble adhering to diet as ages
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Provide emotional support !| !|




Genetic counseling !|

,What kind of diet should a child with Galactosemia Follow - Correct answer
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✔lactose free diet; soy formula !| !| !| !|




Calcium supplementation. !| !|




Dark green leafy green veggies are good
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Can galactosemia breastfeed? - Correct answer ✔NO!!! AVOID!!! Need soy
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formula and calcium supplementation
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Long-term consequences if diet not followed for galactosemia - Correct
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answer ✔learning disabilities, lower IQs, short attention span, behavior
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problems



Clinical Manifestations of galactosemia - Correct answer ✔vomiting, weight
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loss, jaundice (hepatomegaly), lethargy, hypotonia, cataracts (galactose
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accumulation)



When should growth hormone be given? - Correct answer ✔NIGHT TIME!!!
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Sub Q injections given @ night 5x a week. Is stopped once when child is
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where they are supposed to be height wise.
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Realistic expectations for Growth hormone - Correct answer ✔Growth
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hormone will only make them grow to what they were supposed to grow. So
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giving it to them won't make them a 7'0 Center for UK.
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,Nursing considerations for Growth Hormone therapy - Correct answer
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✔serial blood draws q 30 minutes for 3-hours following stimulation with
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insulin or glycogen.
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Treat with chronological age not developmental age
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Incomplete puberty - Correct answer ✔Premature thelarche
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Premature pubarche !|




What is considered True or complete precocious puberty - Correct answer
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✔When Puberty HAPPENS EARLY!!!
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What drug is for Precocious puberty - Correct answer ✔Lupron. Slows
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prepubertal growth to normal rates !| !| !| !|




Given IM monthly
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When to Stop Lupron Treatment - Correct answer ✔Treatment is
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discontinued at age for normal pubertal changes to resume !| !| !| !| !| !| !| !|




Precocious Puberty - Correct answer ✔a condition in which puberty begins
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before the age of 8 in girls and 9 in boys. Testicular enlargement in boys and
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breast enlargement in girls 1st sign
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What drug is used for Treatment of CAH - Correct answer ✔Cortisone to
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suppress abnormally high secretion of ACTH for LIFE. Reconstructive
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surgery as required. !| !|

, What is something a person with CAH should always be wearing? - Correct
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answer ✔Medical alert Bracelet
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Detection of CAH in males - Correct answer ✔precocious genital
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development



Detection of CAH in females - Correct answer ✔-Enlarged clitoris appears as
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a small phallus
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-Fused labia produce saclike structure without testes
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-Internal female sexual organs are intact
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Diagnostic Evaluation for CAH - Correct answer ✔-Ultrasonography to
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visualize pelvic organs !| !|




-Chromosome typing for positive sex determination and to rule out any other
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genetic anomalies !|




Teaching for CAH - Correct answer ✔Teach parents signs and symptoms of
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dehydration and salt-losing crises. Have injectable hydrocortisone available
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and teach how to use it. MONITOR FOR HYPONATREMIC
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DEHYDRATION!!!



Nursing considerations for CAH - Correct answer ✔Hyponatremic
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dehydration for CAH most at risk, sodium less than 135, blood sugar drops,
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do an ultra sound for gender, genetics for CAH status, always have to have
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cortisol replacement. !|