What is a common indirect sign of coarctation of the aorta? - (correct answer) -
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
Right ventricular diameter greater than left ventricular diameter
ghgh gh gh gh gh gh gh gh
And indirect sign of narrowing of the aorta is right, ventricle to left ventricle disprop
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
ortion with the right ventricle, larger than the left ventricle caused by decreased flo
gh gh gh gh gh gh gh gh gh gh gh gh gh
w in the aorta
gh gh gh
Which type of univentricular heart is most lethal?
gh gh gh gh gh gh gh
A. Type A gh gh
B. Туре B gh gh
C. Type C gh gh
D. Type D gh gh
E. Type E - (correct answer) - Type C - absent or rudimentary ventricular septum
gh gh gh gh gh gh ghgh gh gh gh gh gh gh gh
In total anomalous pulmonary venous return (TAPVR) there will always be -
gh gh gh gh gh gh gh gh gh gh gh
(correct answer) - an atrial septal defect and a right-to-left shunt at the atrial level
gh gh gh ghgh gh gh gh gh gh gh gh gh gh gh gh
What is the most common type of total anomalous pulmonary venous return (TAPV
gh gh gh gh gh gh gh gh gh gh gh gh
R)? - (correct answer) - Supracardiac.
gh gh gh gh ghgh
The supracardiac type of total anomalous pulmonary venous return (TAPVR) occurs
gh gh gh gh gh gh gh gh gh gh gh
most frequently, accounting for approximately 44% of cases.
gh gh gh gh gh gh gh
Infracardiac partial anomalous pulmonary venous connection is associated with:
gh gh gh gh gh gh gh gh
A. Shone syndrome
gh gh
B. Scimitar syndrome
gh gh
C. Cor triatriatum
gh gh
D. Situs inversus
gh gh
E. Heterotaxy syndrome - (correct answer) - B. Scimitar syndrome.
gh gh gh gh gh gh ghgh gh gh
Anomalous venous drainage of the right lower and middle lobes occurring in associ
gh gh gh gh gh gh gh gh gh gh gh gh
ation with right lung hypoplasia is termed the scimitar syndrome. One or more of th
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
e puimonary veins drain anomalously into the inferior vena cava, and abnormal art
gh gh gh gh gh gh gh gh gh gh gh gh
erial flow goes into the right lung.
gh gh gh gh gh gh
Partial anomalous pulmonary venous connection from the right lung is almost alwa
gh gh gh gh gh gh gh gh gh gh gh
ys present with:
gh gh
A. Ostium primum atrial septal defect
gh gh gh gh gh
B. Sinus venous atrial septal defect
gh gh gh gh gh
C. Ostium secundum atrial septal defect
gh gh gh gh gh
D. Coronary sinus atrial septal defect
gh gh gh gh gh
,E. Atrioventricular septal defect - (correct answer) -
gh gh gh gh gh gh gh
B. Sinus venosus atrial septal defect
ghgh gh gh gh gh gh
One of the first signs of total anomalous pulmonary venous return (TAPVR) in the fe
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
tus IS: gh
A. Enlarged right ventricle
gh gh gh
B. Prominent pulmonary artery
gh gh gh
C. Enlarged left ventricle
gh gh gh
D. Both A and B
gh gh gh gh
E. All of the above - (correct answer) -
gh gh gh gh gh gh gh gh
D. Both A (enlarged right ventricle) and B (prominent pulmonary artery).
ghgh gh gh gh gh gh gh gh gh gh gh
Diagnosis of total anomalous pulmonary venous return (TAPVR) in the fetus is very
gh gh gh gh gh gh gh gh gh gh gh gh gh
difficult. The right ventricle and pulmonary artery will be enlarged due to increased
gh gh gh gh gh gh gh gh gh gh gh gh gh
blood flow into the right heart. The pulmonary veins drain directly or indirectly into
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
the right atrium instead of the left atrium. When enlargement of the right ventricle
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
and pulmonary artery is present, investigation of the pulmonary veins must be perf
gh gh gh gh gh gh gh gh gh gh gh gh
ormed to rule out anomalous pulmonary venous connections.
gh gh gh gh gh gh gh
Which type of total anomalous pulmonary venous return (TAPVR) is almost always
gh gh gh gh gh gh gh gh gh gh gh gh
associated with a severe obstruction? gh gh gh gh
A. Supracardiac
gh
B. Cardiac
gh
C. Infracardiac
gh
D. Mixed anomalous
gh gh
E. Partial anomalous - (correct answer) - C. Infracardiac.
gh gh gh gh gh gh ghgh gh
in almost all cases of infracardiac total anomalous pulmonary venous return (TAPVR
gh gh gh gh gh gh gh gh gh gh gh
) there is some type of obstruction of the venous return to the heart. The obstructio
gh gh gh gh gh gh gh gh gh gh gh gh gh gh gh
n can occur at any level.
gh gh gh gh gh
The cardiac defect found in all cases of total anomalous pulmonary venous return
gh gh gh gh gh gh gh gh gh gh gh gh
(TAPVR) is: gh
A. Atrial septal defect
gh gh gh
B. Ventricular septal defect
gh gh gh
C. Left superior vena cava
gh gh gh gh
D. Right-sided aortic arch
gh gh gh
E. Coarctation of the aorta - (correct answer) - A. Atrial septal defect.
gh gh gh gh gh gh gh gh ghgh gh gh gh
, with total anomalous pulmonary venous return (TAPVR) there is almost always a rig
gh gh gh gh gh gh gh gh gh gh gh gh
ht-to-left shunt--atrial septa/ defect--
gh gh gh
allowing blood to return to the left heart and systemic circulation.
gh gh gh gh gh gh gh gh gh gh
Hypoplasia of the right ventricle most commonly results from:
gh gh gh gh gh gh gh gh
A. Tricuspid stenosis
gh gh
B. Ventricular septal defect
gh gh gh
C. Redundant foramen ovale
gh gh gh
D. Pulmonary atresia with an intact interventricular septum
gh gh gh gh gh gh gh
E. Mitral valve insufficiency - (correct answer) -
gh gh gh gh gh gh gh
D. Pulmonary atresia with an intact interventricular septum
ghgh gh gh gh gh gh gh gh
What cardiac defect is most commonly associated with double-outlet right ventricle
gh gh gh gh gh gh gh gh gh gh
(DORV)?
A. Pulmonary stenosis
gh gh
B. Aortic stenosis
gh gh
C. Tricuspid stenosis
gh gh
D. Mitral stenosis
gh gh
E. Total anomalous pulmonary venous return - (correct answer) -
gh gh gh gh gh gh gh gh gh
A. pulmonary stenosis
ghgh gh gh
The most common embryologic tissue-migration abnormality is:
gh gh gh gh gh gh
A. Double-outlet right ventricle
gh gh gh
B. Tetralogy of Fallot
gh gh gh
C. Pulmonic stenosis with ventricular septal defect
gh gh gh gh gh gh
D. D-transposition of the great arteries
gh gh gh gh gh
E. Truncus arteriosus - (correct answer) - B. Tetralogy of Fallot
gh gh gh gh gh gh ghgh gh gh gh
The most common type of double-outlet right ventricle is: - (correct answer) -
gh gh gh gh gh gh gh gh gh gh gh gh
Double-outlet right ventricle with a subaortic ventricular septal defect
ghgh gh gh gh gh gh gh gh gh
Classic Taussig-Bing heart is a combination of: - (correct answer) -
gh gh gh gh gh gh gh gh gh gh
Subpulmonic ventricular septal defect with side-by-side great vessels.
ghgh gh gh gh gh gh gh gh
The classic Taussig-
gh gh
Bing physiology is like that in transposition of the great arteries postnatally
gh gh gh gh gh gh gh gh gh gh gh
Ebstein's anomaly is associated with what cardiac defect - (correct answer) -
gh gh gh gh gh gh gh gh gh gh gh
Pulmonic stenosis.
ghgh gh
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
Right ventricular diameter greater than left ventricular diameter
ghgh gh gh gh gh gh gh gh
And indirect sign of narrowing of the aorta is right, ventricle to left ventricle disprop
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
ortion with the right ventricle, larger than the left ventricle caused by decreased flo
gh gh gh gh gh gh gh gh gh gh gh gh gh
w in the aorta
gh gh gh
Which type of univentricular heart is most lethal?
gh gh gh gh gh gh gh
A. Type A gh gh
B. Туре B gh gh
C. Type C gh gh
D. Type D gh gh
E. Type E - (correct answer) - Type C - absent or rudimentary ventricular septum
gh gh gh gh gh gh ghgh gh gh gh gh gh gh gh
In total anomalous pulmonary venous return (TAPVR) there will always be -
gh gh gh gh gh gh gh gh gh gh gh
(correct answer) - an atrial septal defect and a right-to-left shunt at the atrial level
gh gh gh ghgh gh gh gh gh gh gh gh gh gh gh gh
What is the most common type of total anomalous pulmonary venous return (TAPV
gh gh gh gh gh gh gh gh gh gh gh gh
R)? - (correct answer) - Supracardiac.
gh gh gh gh ghgh
The supracardiac type of total anomalous pulmonary venous return (TAPVR) occurs
gh gh gh gh gh gh gh gh gh gh gh
most frequently, accounting for approximately 44% of cases.
gh gh gh gh gh gh gh
Infracardiac partial anomalous pulmonary venous connection is associated with:
gh gh gh gh gh gh gh gh
A. Shone syndrome
gh gh
B. Scimitar syndrome
gh gh
C. Cor triatriatum
gh gh
D. Situs inversus
gh gh
E. Heterotaxy syndrome - (correct answer) - B. Scimitar syndrome.
gh gh gh gh gh gh ghgh gh gh
Anomalous venous drainage of the right lower and middle lobes occurring in associ
gh gh gh gh gh gh gh gh gh gh gh gh
ation with right lung hypoplasia is termed the scimitar syndrome. One or more of th
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
e puimonary veins drain anomalously into the inferior vena cava, and abnormal art
gh gh gh gh gh gh gh gh gh gh gh gh
erial flow goes into the right lung.
gh gh gh gh gh gh
Partial anomalous pulmonary venous connection from the right lung is almost alwa
gh gh gh gh gh gh gh gh gh gh gh
ys present with:
gh gh
A. Ostium primum atrial septal defect
gh gh gh gh gh
B. Sinus venous atrial septal defect
gh gh gh gh gh
C. Ostium secundum atrial septal defect
gh gh gh gh gh
D. Coronary sinus atrial septal defect
gh gh gh gh gh
,E. Atrioventricular septal defect - (correct answer) -
gh gh gh gh gh gh gh
B. Sinus venosus atrial septal defect
ghgh gh gh gh gh gh
One of the first signs of total anomalous pulmonary venous return (TAPVR) in the fe
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
tus IS: gh
A. Enlarged right ventricle
gh gh gh
B. Prominent pulmonary artery
gh gh gh
C. Enlarged left ventricle
gh gh gh
D. Both A and B
gh gh gh gh
E. All of the above - (correct answer) -
gh gh gh gh gh gh gh gh
D. Both A (enlarged right ventricle) and B (prominent pulmonary artery).
ghgh gh gh gh gh gh gh gh gh gh gh
Diagnosis of total anomalous pulmonary venous return (TAPVR) in the fetus is very
gh gh gh gh gh gh gh gh gh gh gh gh gh
difficult. The right ventricle and pulmonary artery will be enlarged due to increased
gh gh gh gh gh gh gh gh gh gh gh gh gh
blood flow into the right heart. The pulmonary veins drain directly or indirectly into
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
the right atrium instead of the left atrium. When enlargement of the right ventricle
gh gh gh gh gh gh gh gh gh gh gh gh gh gh
and pulmonary artery is present, investigation of the pulmonary veins must be perf
gh gh gh gh gh gh gh gh gh gh gh gh
ormed to rule out anomalous pulmonary venous connections.
gh gh gh gh gh gh gh
Which type of total anomalous pulmonary venous return (TAPVR) is almost always
gh gh gh gh gh gh gh gh gh gh gh gh
associated with a severe obstruction? gh gh gh gh
A. Supracardiac
gh
B. Cardiac
gh
C. Infracardiac
gh
D. Mixed anomalous
gh gh
E. Partial anomalous - (correct answer) - C. Infracardiac.
gh gh gh gh gh gh ghgh gh
in almost all cases of infracardiac total anomalous pulmonary venous return (TAPVR
gh gh gh gh gh gh gh gh gh gh gh
) there is some type of obstruction of the venous return to the heart. The obstructio
gh gh gh gh gh gh gh gh gh gh gh gh gh gh gh
n can occur at any level.
gh gh gh gh gh
The cardiac defect found in all cases of total anomalous pulmonary venous return
gh gh gh gh gh gh gh gh gh gh gh gh
(TAPVR) is: gh
A. Atrial septal defect
gh gh gh
B. Ventricular septal defect
gh gh gh
C. Left superior vena cava
gh gh gh gh
D. Right-sided aortic arch
gh gh gh
E. Coarctation of the aorta - (correct answer) - A. Atrial septal defect.
gh gh gh gh gh gh gh gh ghgh gh gh gh
, with total anomalous pulmonary venous return (TAPVR) there is almost always a rig
gh gh gh gh gh gh gh gh gh gh gh gh
ht-to-left shunt--atrial septa/ defect--
gh gh gh
allowing blood to return to the left heart and systemic circulation.
gh gh gh gh gh gh gh gh gh gh
Hypoplasia of the right ventricle most commonly results from:
gh gh gh gh gh gh gh gh
A. Tricuspid stenosis
gh gh
B. Ventricular septal defect
gh gh gh
C. Redundant foramen ovale
gh gh gh
D. Pulmonary atresia with an intact interventricular septum
gh gh gh gh gh gh gh
E. Mitral valve insufficiency - (correct answer) -
gh gh gh gh gh gh gh
D. Pulmonary atresia with an intact interventricular septum
ghgh gh gh gh gh gh gh gh
What cardiac defect is most commonly associated with double-outlet right ventricle
gh gh gh gh gh gh gh gh gh gh
(DORV)?
A. Pulmonary stenosis
gh gh
B. Aortic stenosis
gh gh
C. Tricuspid stenosis
gh gh
D. Mitral stenosis
gh gh
E. Total anomalous pulmonary venous return - (correct answer) -
gh gh gh gh gh gh gh gh gh
A. pulmonary stenosis
ghgh gh gh
The most common embryologic tissue-migration abnormality is:
gh gh gh gh gh gh
A. Double-outlet right ventricle
gh gh gh
B. Tetralogy of Fallot
gh gh gh
C. Pulmonic stenosis with ventricular septal defect
gh gh gh gh gh gh
D. D-transposition of the great arteries
gh gh gh gh gh
E. Truncus arteriosus - (correct answer) - B. Tetralogy of Fallot
gh gh gh gh gh gh ghgh gh gh gh
The most common type of double-outlet right ventricle is: - (correct answer) -
gh gh gh gh gh gh gh gh gh gh gh gh
Double-outlet right ventricle with a subaortic ventricular septal defect
ghgh gh gh gh gh gh gh gh gh
Classic Taussig-Bing heart is a combination of: - (correct answer) -
gh gh gh gh gh gh gh gh gh gh
Subpulmonic ventricular septal defect with side-by-side great vessels.
ghgh gh gh gh gh gh gh gh
The classic Taussig-
gh gh
Bing physiology is like that in transposition of the great arteries postnatally
gh gh gh gh gh gh gh gh gh gh gh
Ebstein's anomaly is associated with what cardiac defect - (correct answer) -
gh gh gh gh gh gh gh gh gh gh gh
Pulmonic stenosis.
ghgh gh