NUR 2356 CORRECT TEST PAPER QUESTIONS AND
ANSWERS SET A+
✔✔Therapeutic management of vaso-occlusive crisis - ✔✔-pain control
-hydration
-rest
-increase tissue perfusion
-treat infection
✔✔Pharmacological and non pharmacological pain control measures for sickle cell
anemia - ✔✔-Opiates (PCA pump)
-NSAIDS
-Around the clock
-Acetaminophen
-Warm compresses
-Guided imagery
-Distraction
-Relaxation
✔✔Why is adequate hydration so important in children with sickle cell anemia -
✔✔Dehydration can cause sickling and clumping of cells, keeps the kidneys working
well, and reduced incidence of stroke
✔✔What teaching can you do related to hydration? - ✔✔-how much fluid they should
get and then more
-Drink on commercial breaks
-drinking games
✔✔Define acute chest syndrome and what is it most commonly caused by - ✔✔A life
threatening complication caused by vascular occlusion in the lungs
(Sickling of blood in lungs)
,caused by bacterial pneumonia - esp streptococcus pneumoniae
✔✔A patient with sickle cell anemia presents to the hospital with chest pain, fever,
tachypnea, coughing, and/or wheezing. What syndrome would you expect them to be
in? - ✔✔Acute chest syndrome
✔✔What diagnostic tests would be ordered to determine acute chest syndrome - ✔✔-
Chest x-ray
-blood culture and sensitivity (from bacterial pneumonia)
✔✔How would a nurse treat a patient with acute chest syndrome - ✔✔-Aggresive
antibiotic therapy (from bacterial pneumonia)
-supplemental O2 PRN
-pain management
✔✔What surgical procedure may be required for a patient with sickle cell who presents
with chronic massive splenomegaly, severe anemia, neutropenia, and
thrombocytopenia? - ✔✔Splenectomy
✔✔Why are blood transfusions (Packed RBCs or Exchange transfusion) used as a
treatment for sickle cell anemia? - ✔✔-Improves tissue oxygenation
-Corrects anemia
-Temporarily reduces the % of HbS
✔✔What is Beta-Thalassemia? - ✔✔An inherited disorder characterized by less
hemoglobin and fewer red blood cells in the body than normal.
✔✔What is beta thalassemia minor (AKA: thalassemia trait) - ✔✔-Produces hypo-
chromic (pale) and microcytic (small) RBCs
-Hgb levels 2-3g/dL below normal levels
✔✔What is beta thalassemia intermediate (AKA: thalassemia intermedia) manifested
as? - ✔✔Manifested as splenomegaly and severe anemia
✔✔What is beta thalassemia major (AKA: Thalassemia major)? And what is it also
known as? - ✔✔Severe complications and requires transfusions to sustain life (Hgb falls
below 5g/dL)
AKA Cooley's Anemia
✔✔A patient presents to the hospital with findings of anemia, characteristic facies
(Distinctive facial features), osteoporosis, epistaxis (nose bleed), and damage to many
organs of the body. What condition could they have? - ✔✔Beta-Thalassemia
, ✔✔What are the 3 consequences and their definitions of the hemolysis of RBCs? -
✔✔1.anemia
2.hemosiderosis - excess iron stores in various tissues of the body but with no tissue
damage
3.hemochromatosis - excess iron storage with cellular damage
✔✔What are the benefits of hypertransfusion therapy for beta-thalassemia - ✔✔-
suppresses extra medullary erythropoiesis
-minimizes facial alterations
-decreses the risk of osteoporosis
-reduces the possibility of splenectomy
-lessens cardiac dilation
(basically the opposite of the clinical manifestations)
✔✔What are 4 other treatment measures (besides hyper transfusion) for beta-
thalassemia - ✔✔1. iron chelation therapy with Exjade (deferasirox) and/or Desferal
(deferoxamine)
2. Oral supplementation of vitamin C and avoidance of iron rich foods
3. Splenectomy
4. Bone marrow or stem cell transplants
✔✔Define hemophilia and what are the 2 types - ✔✔A group of hereditary bleeding
disorders that result from a deficiency in specific clotting factors
1. Hemophilia A or "Classic hemophilia" = missing Factor VIII (antihemophilic factor-
AHF)
2. Hemophilia B or "Christmas disease" = missing Factor IX (plasma thromboplastin
component - PTC)
✔✔How is hemophilia diagnosed? - ✔✔-History of bleeding
-X-linked inheritance
-Lab findings
✔✔What lab tests would be ordered on a patient who is suspected to have hemophilia?
- ✔✔Clotting studies - PT, PTT, aPTT, INR
Coagulating factor concentrations
✔✔A patient with hemophilia is placed on what precautions and what are the goals
when they are hospitalized and at home? - ✔✔Bleeding precautions/ prevention of
bleeding
Hospitalized
ANSWERS SET A+
✔✔Therapeutic management of vaso-occlusive crisis - ✔✔-pain control
-hydration
-rest
-increase tissue perfusion
-treat infection
✔✔Pharmacological and non pharmacological pain control measures for sickle cell
anemia - ✔✔-Opiates (PCA pump)
-NSAIDS
-Around the clock
-Acetaminophen
-Warm compresses
-Guided imagery
-Distraction
-Relaxation
✔✔Why is adequate hydration so important in children with sickle cell anemia -
✔✔Dehydration can cause sickling and clumping of cells, keeps the kidneys working
well, and reduced incidence of stroke
✔✔What teaching can you do related to hydration? - ✔✔-how much fluid they should
get and then more
-Drink on commercial breaks
-drinking games
✔✔Define acute chest syndrome and what is it most commonly caused by - ✔✔A life
threatening complication caused by vascular occlusion in the lungs
(Sickling of blood in lungs)
,caused by bacterial pneumonia - esp streptococcus pneumoniae
✔✔A patient with sickle cell anemia presents to the hospital with chest pain, fever,
tachypnea, coughing, and/or wheezing. What syndrome would you expect them to be
in? - ✔✔Acute chest syndrome
✔✔What diagnostic tests would be ordered to determine acute chest syndrome - ✔✔-
Chest x-ray
-blood culture and sensitivity (from bacterial pneumonia)
✔✔How would a nurse treat a patient with acute chest syndrome - ✔✔-Aggresive
antibiotic therapy (from bacterial pneumonia)
-supplemental O2 PRN
-pain management
✔✔What surgical procedure may be required for a patient with sickle cell who presents
with chronic massive splenomegaly, severe anemia, neutropenia, and
thrombocytopenia? - ✔✔Splenectomy
✔✔Why are blood transfusions (Packed RBCs or Exchange transfusion) used as a
treatment for sickle cell anemia? - ✔✔-Improves tissue oxygenation
-Corrects anemia
-Temporarily reduces the % of HbS
✔✔What is Beta-Thalassemia? - ✔✔An inherited disorder characterized by less
hemoglobin and fewer red blood cells in the body than normal.
✔✔What is beta thalassemia minor (AKA: thalassemia trait) - ✔✔-Produces hypo-
chromic (pale) and microcytic (small) RBCs
-Hgb levels 2-3g/dL below normal levels
✔✔What is beta thalassemia intermediate (AKA: thalassemia intermedia) manifested
as? - ✔✔Manifested as splenomegaly and severe anemia
✔✔What is beta thalassemia major (AKA: Thalassemia major)? And what is it also
known as? - ✔✔Severe complications and requires transfusions to sustain life (Hgb falls
below 5g/dL)
AKA Cooley's Anemia
✔✔A patient presents to the hospital with findings of anemia, characteristic facies
(Distinctive facial features), osteoporosis, epistaxis (nose bleed), and damage to many
organs of the body. What condition could they have? - ✔✔Beta-Thalassemia
, ✔✔What are the 3 consequences and their definitions of the hemolysis of RBCs? -
✔✔1.anemia
2.hemosiderosis - excess iron stores in various tissues of the body but with no tissue
damage
3.hemochromatosis - excess iron storage with cellular damage
✔✔What are the benefits of hypertransfusion therapy for beta-thalassemia - ✔✔-
suppresses extra medullary erythropoiesis
-minimizes facial alterations
-decreses the risk of osteoporosis
-reduces the possibility of splenectomy
-lessens cardiac dilation
(basically the opposite of the clinical manifestations)
✔✔What are 4 other treatment measures (besides hyper transfusion) for beta-
thalassemia - ✔✔1. iron chelation therapy with Exjade (deferasirox) and/or Desferal
(deferoxamine)
2. Oral supplementation of vitamin C and avoidance of iron rich foods
3. Splenectomy
4. Bone marrow or stem cell transplants
✔✔Define hemophilia and what are the 2 types - ✔✔A group of hereditary bleeding
disorders that result from a deficiency in specific clotting factors
1. Hemophilia A or "Classic hemophilia" = missing Factor VIII (antihemophilic factor-
AHF)
2. Hemophilia B or "Christmas disease" = missing Factor IX (plasma thromboplastin
component - PTC)
✔✔How is hemophilia diagnosed? - ✔✔-History of bleeding
-X-linked inheritance
-Lab findings
✔✔What lab tests would be ordered on a patient who is suspected to have hemophilia?
- ✔✔Clotting studies - PT, PTT, aPTT, INR
Coagulating factor concentrations
✔✔A patient with hemophilia is placed on what precautions and what are the goals
when they are hospitalized and at home? - ✔✔Bleeding precautions/ prevention of
bleeding
Hospitalized
