Carnitine Study guides, Class notes & Summaries

Genetic Counseling Boards study guide (latest updates) *Sickle Cell* Genetics Phenotype Diagnosis Treatment - *Genetics:* HbSS Gluexon6Val mutation in HBB gene chr. 11p15.4 *Phenotype:* Structurally abnormal Hb Manifests at 6-12 months (HbF --> HbA) Painful crises, anemia, organ damage, pulmonary HTN *Diagnosis:* Hb electrophoresis *Treatment:* hydroxyurea (stimulates HbF) *Alpha-thalassemia* Genetics Phenotype - *Genetics:* 2 alpha globin genes (4 alleles) chr. 16 *Phe...

What are the primary organic acid abnormalities that occur in carnitine deficiency? correct answers -adipate -suberate -ethylmalonate What patterns of abnormalities discriminate mitochondrial inefficiency from ammonia challenge as a cause of citric acid elevation? correct answers -high citrate, aconitate, isocitrate + orotate indicates ammonia challenges -wihtout orotate= mitochondrial inefficiency What patterns suggest a deficiency of CoQ10? correct answers -High succinate, fumarate, ...

In the fasted state, fatty acyl-CoAs are transported across the mitochondrial membrane. The transport of fatty acids via carnitine palmitoyl transferase 1 can be directly inhibited by which of the following compounds? correct answer: Malonyl-CoA An individual is on a hunger strike and has not eaten in 13 days. Which of the following best describes their metabolic state? correct answer: The brain will be preferentially oxidizing ketones. Ketonuria, hyperglycemia and severe acidosis are pr...

Biochemistry Final Exam Review Questions And Answers In the fasted state, fatty acyl-CoAs are transported across the mitochondrial membrane. The transport of fatty acids via carnitine palmitoyltransferase I (CPT-1) can be directly inhibited by which of the following compounds? a. Malonyl-CoA b. Carnitine c. Palmitate d. Acetyl-CoA - ANS Malonyl-CoA In the fasted state, fatty acyl-CoAs are transported across the mitochondrial membrane. The transport of fatty acids via carnit...

Vitamins + Minerals - play integral role in cell metabolism Recommendations for essential nutrient intake levels - are established to support optimal function and health The fat-soluble vitamins (soluble in oil) - A; D; E; K The water soluble nutrients - water-soluble B vitamins, thiamin, riboflavin, niacin, vitamin B6, vitamin B12, biotin, pantothenic acid, folate, choline, + water soluble vitamin C Vitamin A - functions in vision (including light and dark adaptation ...

In the liver, which of the following key inhibitory events ensures that newly synthesized palmitoyl-CoA is not immediately oxidized? Carnitine palmitoyl transferase-I (CPTI) by palmitoylcarnitine Carnitine palmitoyl transferase-II (CPTII) by acetyl-CoA Acyl-CoA synthetase by malonyl CoA Carnitine palmitoyl transferase-I (CPTI) by malonyl-CoA Carnitine acylcarnitine translocase (CAT) by palmitoyl-CoA correct answer: Carnitine palmitoyl transferase-I (CPTI) by malonyl-CoA Malony...

davids super cool Davids This One UNE BioChem 1005 Final Exam Questions And Answers Carnitine palmitoyl transferase - ANS - transfers acyl groups from CoA to carnitine & vice versa - inhibited by malonyl-CoA ketone bodies - ANS - acetoacetate, β-hydroxybutyrate, acetone - oxidized as fuel source in extreme fasting d-3-hydroxybutyrate dehydrogenase - ANS interconversion of acetoacetate and 3-hydroxybutyrate acetone - ANS yielded by spontaneous decarboxylation of acet...

NASM Physique and Bodybuilding Coach Exam Questions And Answers Which supplement is believed to help increase the transport of fatty acids into the mitochondria, but may have little actual effect on body fat loss? Select one: a. L-Carnitine b. Caffeine c. Carnosine d. Creatine a. L-Carnitine Periodization does not appear to benefit muscle size changes when equating for which variable between different periodized models? Select one: a. Strength at baseline testing b. Calorie intake c....

Irene Gold Boards Part 1-Biochemistry Exam Questions with 100% Correct Answers How many a.a.'s are incorporated into proteins? - Answer ️️ -20 What structures make up an AA? - Answer ️️ -Amine group Acid group Hydrogen R-Group = defining group All a.a.'s are in L-form EXCEPT for what? - Answer ️️ -glycine Glycine is not in L-form because? - Answer ️️ -it doesn't contain a chiral carbon define chiral carbon - Answer ️️ -different compounds at each binding site All...

Carnitine palmitoyl transferase - ANSWERS- transfers acyl groups from CoA to carnitine & vice versa - inhibited by malonyl-CoA ketone bodies - ANSWERS- acetoacetate, β-hydroxybutyrate, acetone - oxidized as fuel source in extreme fasting d-3-hydroxybutyrate dehydrogenase - ANSWERSinterconversion of acetoacetate and 3-hydroxybutyrate acetone - ANSWERSyielded by spontaneous decarboxylation of acetoacetate; waste product acetoacetate and 3-hydroxybutyrate - ANSWERS- ketone bodies pro...