CYSTIC FIBROSIS - MUTATED CFTR GENE LATEST
UPDATE 2025/2026 WITH 100% ACCURATE
QUESTIONS AND ANSWERS 100% A+ GUARANTEE
CF oral drugs that help fix cause ?-CORRECT ANSWERKaftrio (Elexacaftor, Tezacaftor, Ivacaftor)
Oral drugs given solo ?-CORRECT ANSWERIvacaftor (kalydeco) given solo.
Oral Drug prescribed under a Managed Access Scheme (as drug effectiveness is being established there
is an agreement between NHS & manufacturers )-CORRECT ANSWEROrkambi (lumacaftor & ivacaftor)
If CF patients have exocrine pancreatic insufficiency what drug give ?-CORRECT ANSWERPancreatin
supplements before food
What is PEP? -CORRECT ANSWERPositive Expiratory Pressure (Physio intervention device)
CF drugs available under managed access scheme ? -CORRECT ANSWERLumacaftor & Ivacaftor
(Orkambi)
UPDATE 2025/2026 WITH 100% ACCURATE
QUESTIONS AND ANSWERS 100% A+ GUARANTEE
CF oral drugs that help fix cause ?-CORRECT ANSWERKaftrio (Elexacaftor, Tezacaftor, Ivacaftor)
Oral drugs given solo ?-CORRECT ANSWERIvacaftor (kalydeco) given solo.
Oral Drug prescribed under a Managed Access Scheme (as drug effectiveness is being established there
is an agreement between NHS & manufacturers )-CORRECT ANSWEROrkambi (lumacaftor & ivacaftor)
If CF patients have exocrine pancreatic insufficiency what drug give ?-CORRECT ANSWERPancreatin
supplements before food
What is PEP? -CORRECT ANSWERPositive Expiratory Pressure (Physio intervention device)
CF drugs available under managed access scheme ? -CORRECT ANSWERLumacaftor & Ivacaftor
(Orkambi)