ACTUAL Exam Questions and CORRECT
Answers
vascular/extravascular disorders are characterized by - CORRECT ANSWER - disorders
of blood vessels or tissues surrounding vessels
causes of vascular/extravascular disorders - CORRECT ANSWER - defect in the structure
or function of the vascular endothelium or sub endothelium (collagen)
bleeding time results in vascular disorders - CORRECT ANSWER - prolonged
vascular disorders: capillary fragility results - CORRECT ANSWER - positive
vascular disorders: plt count - CORRECT ANSWER - normal
vascular disorders: PT, PTT - CORRECT ANSWER - normal
list 3 aquired vascular disorders - CORRECT ANSWER - 1. senile purpura
2. simple easy bruising
3. secondary vascular purpura
some causes of secondary vascular purpura - CORRECT ANSWER - secondary damage to
endothelium due to immune deficiency, vit C deficiency
main characteristic of inherited vascular disorders - CORRECT ANSWER - disordered
collagen
, main characteristic of hereditary hemorrhagic telangiectasia (HHT) - CORRECT
ANSWER - dilations of capillaries
ehler-danlos syndrome - CORRECT ANSWER - loss of elasticity in the epidermis and
sub-epidermal tissues (deformable skin)
marfans syndrome - CORRECT ANSWER - abnormal fibrillin in connective tissue
osteogenesis imperfecta - CORRECT ANSWER - defective collagen formation, brittle
bones
homocystinuria - CORRECT ANSWER - amino acid disoders
pseudo xanthoma elasticum - CORRECT ANSWER - disorder of elastin in which elastic
tissues mineralize
2 classifications of platelet disorders - CORRECT ANSWER - 1. quantitative (numbers
2. qualitative (function)
thrombocytopenia - CORRECT ANSWER - decreased platelet count; critical <20 x
10^9/L
thrombocytosis - CORRECT ANSWER - increased platelet count
thrombocythemia - CORRECT ANSWER - extreme increased platelet count >1000 x
10^9/L
thrombocytopenia: platelet count - CORRECT ANSWER - decreased