RC 329 EXAM 2 QUESTIONS AND
ANSWERS 2026 VERIFIED.
Define the following types of bronchiectasis with descriptions of their shapes.
1. cylindrical
2. varicose
3. cystic - ANS 1. uniform dilation of the airways
2. alternating constriction and dilation
3. progressive enlargement of airways resembling sacks
True or False: A positive screening immunoreactive trypsinogen test (on newborn screen)
indicates a need for a sweat chloride test. - ANS true
T or F: CF is primarily a restrictive lung disease. - ANS false
T or F: CF related bronchiectasis is rarely found until after the first decade of life. - ANS false,
can be found as early as 3 months of age
T or F: Inhaled steroids are highly effective and frequently used as anti-inflammatory agents in
CF. - ANS false
What is the most common inhaled antibiotic used to treat pseudomonas in CF? -
ANS tobramycin
@COPYRIGHT ALL RIGHTS RESERVED PAGE 1 OF 13
, List 3 CFTR modulator drugs in current use. - ANS elexacaftor, ivacafotr, tezacaftor
Which of the following disorders/diseases are often associated with cystic fibrosis?
1. Rheumatoid Arthritis
2. Hypertension
3. Chronic Kidney Disease
4. Nasal Polyps
5. Diabetes
6. Infertility
7. Liver Disease - ANS 4, 5, 6 and 7
Which of the following is the most common cause of bronchiectasis?
1. Recurrent lung infections
2. Aspiration from GERD
3. Dust inhalation
4. Autoimmune disorders - ANS 1
What are some common disorders/diseases associated with cystic fibrosis? -
ANS bronchiectasis, malnutrition, diabetes, pancreatic insufficiency, nasal polyps, liver
disease, chronic infections
Describe the typical RT regimen for CF patients in the hospital - ANS Bronchodilator,
hypertonic saline, ACT, mucolytic, antibiotcis (tobi or coli), steroids, CFTR modulators, oxygen if
needed
How does optimal patient positioning in severe liver disease compare to optimal positioning in
CHF? - ANS - liver disease patients have platypnea and feel dyspneic when upright because of
ascites and portal hypertension
- heart failure patients have orthopnea which means they become dyspneic when laying down
when fluid built up in the extrememties returns to the abdomen
@COPYRIGHT ALL RIGHTS RESERVED PAGE 2 OF 13
ANSWERS 2026 VERIFIED.
Define the following types of bronchiectasis with descriptions of their shapes.
1. cylindrical
2. varicose
3. cystic - ANS 1. uniform dilation of the airways
2. alternating constriction and dilation
3. progressive enlargement of airways resembling sacks
True or False: A positive screening immunoreactive trypsinogen test (on newborn screen)
indicates a need for a sweat chloride test. - ANS true
T or F: CF is primarily a restrictive lung disease. - ANS false
T or F: CF related bronchiectasis is rarely found until after the first decade of life. - ANS false,
can be found as early as 3 months of age
T or F: Inhaled steroids are highly effective and frequently used as anti-inflammatory agents in
CF. - ANS false
What is the most common inhaled antibiotic used to treat pseudomonas in CF? -
ANS tobramycin
@COPYRIGHT ALL RIGHTS RESERVED PAGE 1 OF 13
, List 3 CFTR modulator drugs in current use. - ANS elexacaftor, ivacafotr, tezacaftor
Which of the following disorders/diseases are often associated with cystic fibrosis?
1. Rheumatoid Arthritis
2. Hypertension
3. Chronic Kidney Disease
4. Nasal Polyps
5. Diabetes
6. Infertility
7. Liver Disease - ANS 4, 5, 6 and 7
Which of the following is the most common cause of bronchiectasis?
1. Recurrent lung infections
2. Aspiration from GERD
3. Dust inhalation
4. Autoimmune disorders - ANS 1
What are some common disorders/diseases associated with cystic fibrosis? -
ANS bronchiectasis, malnutrition, diabetes, pancreatic insufficiency, nasal polyps, liver
disease, chronic infections
Describe the typical RT regimen for CF patients in the hospital - ANS Bronchodilator,
hypertonic saline, ACT, mucolytic, antibiotcis (tobi or coli), steroids, CFTR modulators, oxygen if
needed
How does optimal patient positioning in severe liver disease compare to optimal positioning in
CHF? - ANS - liver disease patients have platypnea and feel dyspneic when upright because of
ascites and portal hypertension
- heart failure patients have orthopnea which means they become dyspneic when laying down
when fluid built up in the extrememties returns to the abdomen
@COPYRIGHT ALL RIGHTS RESERVED PAGE 2 OF 13
