- REBECCA CLARK-BASH STUDY
SET 2026 ACTUAL QUESTIONS WITH
VERIFIED ANSWERS.
What are some symptoms of Herpes Simplex Encephalitis? -
correct answer-Aphasia, Confusion & Behavioral Changes
What EEG changes are associated with Herpes Simplex
Encephalitis? - correct answer-Focal slowing, spiking, and
paroxysmal lateralizing epileptiform discharges
Is Herpes Simplex Encephalitis potentially fatal? - correct
answer-Yes
What is Rasmussen's Encephalitis? - correct answer-A rare,
chronic inflammatory disease that usually affects only one
hemisphere of the brain.
,Who does Rasmussen's Encephalitis primarily affect? - correct
answer-Children under the age of 10, and more rarely in
adolescents and adults.
What are the main symptoms of Rasmussen's Encephalitis? -
correct answer-Frequent and severe seizures, loss of motor
skills and speech, paralysis on one side of the body,
inflammation of the brain, and mental deterioration.
What is the believed cause of Rasmussen's Encephalitis? -
correct answer-An autoimmune disease in which immune
system cells enter the brain, causing inflammation and
damage.
Severe myoclonic epilepsy of infancy
Rare
Intractable Epilepsy
Behavioral & Developmental Delays
Risk of SUDEP - correct answer-Dravets Syndrome
,What is Rett Syndrome? - correct answer-A disorder of the
nervous system that leads to developmental reversals,
especially in the areas of expressive language and hand use.
What is the typical developmental pattern in infants with Rett
Syndrome? - correct answer-Infants usually have normal
development for the first 6-18 months.
How does the severity of Rett Syndrome vary? - correct
answer-The syndrome ranges from mild to severe.
What is the neuro-genetic disorder characterized by intellectual
and developmental delay, sleep disturbances, seizures, jerky
movements, frequent laughter or smiling, and usually a happy
demeanor? - correct answer-Angelmans Syndrome
What are the speech characteristics of individuals with
Angelmans Syndrome? - correct answer-Speech impairment,
no or minimal use of words; receptive and non-verbal
communication skills higher than verbal ones.
Also called Myoclonic Atonic Epilepsy, can also have absence.
, Uncommon childhood epilepsy
Boys greater than girls
Valproic acid first line agent
Frequent generalized spike-wave activity in brief bursts of 2-
5Hz. Background may be normal or abnormal. - correct
answer-Doose Syndrome
What is the congenital brain malformation involving the
cerebellum and the fluid filled spaces around it? - correct
answer-Dandy-Walker Syndrome
What is a key feature of Dandy-Walker Syndrome? - correct
answer-Partial or complete absence of the part of the brain
located between the two cerebellar hemispheres
What is the rare congenital neurological and skin disorder
characterized by port-wine stains of the face, glaucoma,
seizures, mental retardation, and ipsilateral leptomengingeal
angioma? - correct answer-Sturge-Weber syndrome
What is the main feature of Sturge-Weber syndrome related to
the brain's arteries? - correct answer-Proliferation of arteries of
the brain resulting in multiple angiomas