ATI Peds Hematologic Disorders
1. labs for sickle cell crisis: lower Hgb, higher WBC, higher bilirubin & reticulocytelevels
2. sca nursing care: promote rest, admin O2, monitor I&O, give oral fluids, IV too,admin
antibiotics, penicillen, pneumococcal conjugate, meningococcal vacc, hib B
3. SCA pain tx: tylenol, advil, opioids on reg schedule to avoid pain
4. Complications of SCA: cerebrovascular accident and acute chest syndrome
5. CVA mifestations: seizures, abnormal behavior, weakness, slurred speech,visual changes,
vomiting, severe HA
6. Acute chest syndrome: (may look like pneumonia) assess for chest, back or abdom pain,
fever of 38.5 (101.3) higher, cough, tachypnea, dyspnea, retractions,lower O2 saturation
7. Hemophilia: group of bleeding disorders charact by diff controlling bleeding
8. hemophilia bleeding time extends due to: lack of factor required for blood to clot. bleeding
external and internal
9. Kids with SCD have what performed annually (2-16 yo): TCD - TranscranialDoppler
10. Both hemophilia A & B are: x-linked recessive disorders
11. Hemophilia A is deficiency of: factor VIII
12. Hemophilia B is deficiency of: factor IX aka Christmas disease
13. Hemophilia expected findings: episodes of bleeding, excessive bleeding, joint pain and
stiffness, impaired mobiliity, easy bruising and activity intolerance,hematomas, slurred
speech, decreased loc
14. hemophilia lab tests: prolonged PTT, factor-specific assays to determine defi-ciency,
platelets and PT would show normal range,
15. Hemophilia determined by: DNA testing
16. caring for hemophilia patient: admin subcut vs im, avoid aspirin,monitor for occult blood,
assess for ha, chng in hr or bp, encourage rest and apply ice to painfuljoints
17. DDAVP / synthetic form of vasopressin: admin IV, used to prevent and treathemorrhage
18. corticosteroids and nsaids: used to treat hematuria and hemophilia
19. repeated episodes of hemarthrosis leads to: impaired joints, pain-may leadto joint
deformaties
20. RN providing teaching of epistaxis which positions should the rn instructchild when nose
bleeds?: Sit up and lean forward, not head back (aspiration)
21. whats an approp action to take when managing epistaxis?: press narestogether for 10 mins
& pack cotton into bleeding nares
1. labs for sickle cell crisis: lower Hgb, higher WBC, higher bilirubin & reticulocytelevels
2. sca nursing care: promote rest, admin O2, monitor I&O, give oral fluids, IV too,admin
antibiotics, penicillen, pneumococcal conjugate, meningococcal vacc, hib B
3. SCA pain tx: tylenol, advil, opioids on reg schedule to avoid pain
4. Complications of SCA: cerebrovascular accident and acute chest syndrome
5. CVA mifestations: seizures, abnormal behavior, weakness, slurred speech,visual changes,
vomiting, severe HA
6. Acute chest syndrome: (may look like pneumonia) assess for chest, back or abdom pain,
fever of 38.5 (101.3) higher, cough, tachypnea, dyspnea, retractions,lower O2 saturation
7. Hemophilia: group of bleeding disorders charact by diff controlling bleeding
8. hemophilia bleeding time extends due to: lack of factor required for blood to clot. bleeding
external and internal
9. Kids with SCD have what performed annually (2-16 yo): TCD - TranscranialDoppler
10. Both hemophilia A & B are: x-linked recessive disorders
11. Hemophilia A is deficiency of: factor VIII
12. Hemophilia B is deficiency of: factor IX aka Christmas disease
13. Hemophilia expected findings: episodes of bleeding, excessive bleeding, joint pain and
stiffness, impaired mobiliity, easy bruising and activity intolerance,hematomas, slurred
speech, decreased loc
14. hemophilia lab tests: prolonged PTT, factor-specific assays to determine defi-ciency,
platelets and PT would show normal range,
15. Hemophilia determined by: DNA testing
16. caring for hemophilia patient: admin subcut vs im, avoid aspirin,monitor for occult blood,
assess for ha, chng in hr or bp, encourage rest and apply ice to painfuljoints
17. DDAVP / synthetic form of vasopressin: admin IV, used to prevent and treathemorrhage
18. corticosteroids and nsaids: used to treat hematuria and hemophilia
19. repeated episodes of hemarthrosis leads to: impaired joints, pain-may leadto joint
deformaties
20. RN providing teaching of epistaxis which positions should the rn instructchild when nose
bleeds?: Sit up and lean forward, not head back (aspiration)
21. whats an approp action to take when managing epistaxis?: press narestogether for 10 mins
& pack cotton into bleeding nares
