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Test Bank For Pediatrics 19th Edition By Nelson 2024.
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, Test Bank For Pediatrics 19th Edition By Nelson 2024.
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WhichvphasevofvKawasakivdiseasevisvassociatedvwithvcoronaryvaneurysms?
A. Acutevfebrilevphase
B. Subacutevphase
C. Convalescentvphase
D. Phasevofvcomplications
E. Allvofvthevabovev-vANSWERv-v1vB.
Kawasakivdiseasevpresentsvwithvcharacteristicallyvhigh,vunremittingvfevervandv4voutvofvthev5vpri
ncipalvfeatures:
Bilateralvnonexudativevbulbarvconjunctivalvinjectionvwithvlimbalvsparing;
Erythemavofvthevoralvandvpharyngealvmucosavwithvstrawberryvtonguevandvdry,vcrackedvlips;v
Edemavandverythemavofvthevhandsvandvfeet;
Rashvofvvariousvformsv(scarlatiniform,vmaculopapular,verythemavmultiforme);vNonsuppurati
vevcervicalvlymphadenopathyv(usuallyvunilateral,vwithvnodevsizev>1.5cm).vAcutevfebrilevphase
v-vfevervandvthevacutevsignsvofvillnessvandvusuallyvlastsv1-2wks
Subacutevfebrilevphasev-
vdesquamation,vthrombocytosis,vcoronaryvaneurysmsvandvhighestvriskvofvsuddenvdeathvusual
lyvlastsv2vwks
Convalescentvphasev-vAllvclinicalvsignsvhavevdisappearedvuntilvESRvnormalizesvtypicallyv6-
v 8wksvaftervonsetvonvillness
Source:vNelson'svTextbookvofvPediatricsv19thveditionvp864
Avfourvyearvoldvpresentsvwithvlow-
gradevfever,vintermittentvcrampyvabdominalvpainvwithvemesisvandvswollenvkneesvofv3vdaysvd
uration.vAvpurpuricvrashvdistributedvbelowvthevkneesvofvbothvlowervextremitiesvisvnotedvonvp
hysicalvexamination.vThisvpatientvmostvlikelyvhas:
A. Meningococcemia
B. Idiopathicvthrombocytopenicvpurpura
C. Henoch-Scholeinvpurpura
D. SLEvE.vJuvenilevRheumatoidvarthritisv-vANSWERv-v2vC.
HSPvisvavcommonvvasculitisvamongvchildrenvandvpresentsvwithvthevclassicvfindingsvofvabdomi
nalvpainvwithvorvwithoutvrectalvbleeding,vvasculitisvrash,varthritisvandvnephritis.vThevplateletv
countvisvnormal.vGastrointestinalvinvolvementvmayvprogressvtovintussusception.
Source:vNelson'svTextbookvofvPediatricsv19thveditionvp868
Av3vyearvoldvfemalevpresentsvwithv1vweekvhistoryvofvdailyv(quotidian)vfevervassociatedvwithv
arthritisvofvbothvanklesvandvhervrightvknee.vHervmothervnotesvthatvshevhasvdecreasedvactivity
Test Bank For Pediatrics 19th Edition By Nelson 2024.
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, Test Bank For Pediatrics 19th Edition By Nelson 2024.
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andvalsovnotesvrashesvthatvcomevandvgovinvdifferentvpartsvofvhervbodyvbutvnotvonvthevface.vOnv
physicalvexamination,vsalmonvcoloredvpatchesvwerevnotedvonvthevtrunkvandvextremities.vPal
pationvrevealedvsplenomegaly.vWhatvisvthevdiagnosis?
A. HenochvSchoenleinvPurpura
B. SystemicvLupusvErythematosus
C. JuvenilevRheumatoidvarthritis
D. JuvenilevDermatomyositis
E. Denguevfeverv-vANSWERv-v3vC.
Don'tvforgetvtovstudyvrheumaticvdiseasesvofvchildhoodvevenvifvit'svnotvyourvfavoritevtopic.vFa
miliarizevyourselfvwithvthevrelativelyvcommonvonesvlikevJRA,vSLEv andvdermatomyositis,v HSP
v andv scleroderma.v Payv attentionv tov thevcharacteristicsv ofv thev rashv andv otherv features.v(Don
'tvfallvforvthevtrapvofvrashv+varthritisv=vSLE..vIt'svnotvalwaysvSLE!)
JRAv-
vSalmonvcoloredvpatch,vevanescent,vsparesvthevfacevSLEv-
vMalarvrash,vphotosensitive
Dermatomyositisv-
vheliotropev(periorbital)vrash,vgottronvpapulesv(rashvonvthevknuckles)vHSPv-
vpurpuravinvdependentvportions
ForvJRA,vknowvthevdifferencesvbetweenvsubtypesv(oligoarticularvvsvpolyarticularvvsvsystemicvons
et)
ThisvcasevinvparticularvisvavcasevofvsystemicvonsetvJuvenilevRheumatoidvarthritisv(alsovcalledvStill
'svDisease)
Source:vNelson'svTextbookvofvPediatricsv19thveditionvp830
Av4vyrvoldvboyvpresentsvwithvhisvthirdvepisodevofvpainfulvcervicalvlymphadenitis.vEachvwasvtr
eatedvwithvincisionvandvdrainagevandvgrewvS.vaureus.vHevalsovexperiencesvrecurrentvskinvinf
ections.vAvyearvago,vhevwasvhospitalizedvforvosteomyelitis.vThevmostvimportantvlaboratoryvte
stvis:
A. PCRvforvADAvdeficiency
B. Nitrobluevtetrazoliumvtest
C. MAC-Ivassay
D. Neutrophilvcount
E. Geneticvchromosomalvanalysisv-vANSWERv-
v4vB.vThisvisvavcasevofvchronicvgranulomatousvdiseasev(CGD)vwhereinvpatientsvarevsusceptiblev
tovcatalasevpositivevorganismsvlikevS.vaureus.vThevnitrobluevtetrazoliumvtestsvthevneutrophilsv
abilityvtovgeneratevsuperoxidevanionvandvthusvkillvingestedvbacteria.
Source:vNelson'svTextbookvofvPediatricsv19thveditionvp746
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, Test Bank For Pediatrics 19th Edition By Nelson 2024.
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WhichvamongvthevfollowingvisvnotvavprominentvfeaturevofvWiskott-Aldrichvsyndrome?
A. X-linkedvrecessivevinheritance
B. Atopicvdermatitis
C. Thrombocytopenia
D. Recurrentvinfectionsvwithvencapsulatedvbacteria
E. Leukopeniav-vANSWERv-v5vE.
Note:v Thev prominentv immunologicv impairmentv inv Wiskottv Aldrichv Syndromev isv againstvpoly
saccharidesvofvencapsulatedvorganisms
Source:vNelson'svTextbookvofvPediatricsv19thveditionvp734
Av12vyearvoldvseeksvconsultvforv1vdayvhistoryvofvsneezing,vclearvrhinorrheavandvnasalvitchingv
notvassociatedvwithvfevervorvanyvothervsystemicvsymptoms.vPEvrevealsvboggy,vpalevnasalvede
mavwithvavclearvdischarge.vThevmostvlikelyvdiagnosisvis?
A. Foreignvbody
B. Vasomotorvrhinitis
C. Allergicvrhinitis
D. Neutrophilicvrhinitis
E. Rhinitisvmedicamentosav-vANSWERv-v6vC.
Allergicv rhinitisv isv oftenv seasonalv andv associatedv withv allergicv conjunctivitis.v Eosinophilsvpre
dominatevinvthevnasalvsecretions.vItvisvclassifiedvas:
Seasonalv(cyclical)vorvperennialv(allvyear)
Intermittentv (symptomsv occurv <4v daysv perv weekv orv <4v consecutivev weeks)v orv persistentv(sy
mptomsvoccurv>4vdaysvpervweekvorv>4vconsecutivevweeks)
Mild-
moderatev(novimpairment)vorvseverev(withvimpairmentvofvdailyvliving/sleep)vSource:vNel
son'svTextbookvofvPediatricsv19thveditionvp775
ThevKasaivprocedurevisvindicatedvforvwhichvofvthevfollowing?
A. Neonatalvhepatitis
B. Biliaryvatresia
C. Metabolicvlivervdisease
D. Fulminantvhepaticvfailure
E. Nonevofvthevabovev-vANSWERv-v7vB.
DespitevinitialvsuccessvofvthevKasaivoperation,vpatientsvwithvbiliaryvatresiaveventuallyvgetvlivervtra
nsplantation.
Source:vNelson'svTextbookvofvPediatricsv19thveditionv1387
Test Bank For Pediatrics 19th Edition By Nelson 2024.
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