Study Guide CLTM Quiz 6 actual exam questions and answers

Sturge-Weber Syndrome Which neurological disorder is characterized by a port wine stain? Define: Agnosia inability to recognize objects, people, sounds, shapes or smells; symptom common to tumors of the parietal lobes Define: Anosmia loss of sense of smell Define: Apraxia The inability to execute voluntary and purposeful motor movements Landau-Kleffner Syndrome ESES is associated with which disorder? Todd's paralysis Temporary postictal paralysis Gelastic seizures Hypothalamus hamartomas are associated with with disorder? Mesial temporal lobe epilepsy What is the most common form of temporal lobe epilepsy? Jeavon's Syndrome Eyelid myoclonia with absences, eye closure induced seizures, EEG paroxysms and photosensitivity Mesial temporal lobe epilepsy What is the most common form of focal epilepsy? 3 Hz spike and wave What would you expect to see on an EEG of a patient with CAE? Ethosuximide, Valproate, Lamotrigine What medications would be used to treat CAE? 10 -16 yrs old What is the average age of onset of JAE? Generalized poly spike or spike and wave discharges at 3 -4 Hz What would you expect to see on an EEG of a patient with JAE? 3 -13 yrs old What is the onset age for patients with BECTS? True T or F: Most children are not medicated with BECTS Panayiotopoulos Syndrome An early Onset Benign Occipital Epilepsy/syndrome that typically has seizures that are nocturnal with vomiting and nausea? 1 -18 months What is the typical age of onset for Dravet Syndrome? False T or F: Sodium channel blockers are the first-line medication recommended for Dravet Syndrome. GTC, Myoclonic, and Absence What seizure types would you expect to see in Juvenile Myoclonic Epilepsy? True T or F: Males are more often affected by Landau-Kleffner Syndrome than females Multiple subpial transections What surgery may be an option for Landau-Kleffner Syndrome sufferers? Corpus Callostomy What surgery option is available for those suffering from Lennox-Gastaut Syndrome? Tonic, Atonic, Atypical absence, Myoclonic, Generalized tonic-clonic, and Focal seizures What type of seizures may be even in a patient with Lenox-Gastaut Syndrome? Infantile spasms West Syndrome <1 yr old What is the typical onset for symptoms for West Syndrome? Hypsarrhythmia What would you expect to see on an EEG of a patient with West Syndrome? Tuberous sclerosis complex What is the most common disorder for West Syndrome? ACTH injections First line medication for West Syndrome. Reflex epilepsies What type of epilepsy can be triggered by something in the environment? Rasmussen Syndrome Rare disorder of the CNS characterized by encephalitis of one cerebral hemisphere Cerebral hemispherectomy What surgery option is available for those suffering from Rasmussen Syndrome? Hippocampal sclerosis Mesial temporal lobe epilepsy