Nur 311 Exam 2 Study Guide Practice
Questions With Correct Answers
PKU diet to follow - CORRECT ANSWER✔✔-Breast Feeding or PA+ Free
| | | | | | | | | | |
Formula. Restricted PA + Intake Throughout Life; No meat, limited fruits
| | | | | | | | | | |
& vegetables, limited grains
| | |
What happens if people with PKU don't follow their diet - CORRECT
| | | | | | | | | | | |
ANSWER✔✔-Short Attention Span | |
Poor short term memory
| | |
Visual perception problems
| |
Poor motor coordination
| | |
Mood disorders |
Brain structural changes (reduced grey matter)
| | | | |
Safe PKU level - CORRECT ANSWER✔✔-2-6mg/dl
| | | | |
PKU nursing Considerations - CORRECT ANSWER✔✔-Assist with testing
| | | | | | |
Teach parents about diet and need for follow up blood levels
| | | | | | | | | | |
throughout life |
Child may have trouble adhering to diet as ages
| | | | | | | |
,Provide emotional support | |
Genetic counseling |
What kind of diet should a child with Galactosemia Follow - CORRECT
| | | | | | | | | | | |
ANSWER✔✔-lactose free diet; soy formula | | | |
Calcium supplementation. | |
Dark green leafy green veggies are good
| | | | | |
Can galactosemia breastfeed? - CORRECT ANSWER✔✔-NO!!! AVOID!!!
| | | | | | |
Need soy formula and calcium supplementation
| | | | |
Long-term consequences if diet not followed for galactosemia -
| | | | | | | | |
CORRECT ANSWER✔✔-learning disabilities, lower IQs, short attention
| | | | | | |
span, behavior problems
| |
Clinical Manifestations of galactosemia - CORRECT ANSWER✔✔-
| | | | | |
vomiting, weight loss, jaundice (hepatomegaly), lethargy, hypotonia,
| | | | | | |
cataracts (galactose accumulation)
| |
When should growth hormone be given? - CORRECT ANSWER✔✔-
| | | | | | | |
NIGHT TIME!!! Sub Q injections given @ night 5x a week. Is stopped
| | | | | | | | | | | | |
once when child is where they are supposed to be height wise.
| | | | | | | | | | |
,Realistic expectations for Growth hormone - CORRECT ANSWER✔✔-
| | | | | | |
Growth hormone will only make them grow to what they were
| | | | | | | | | | |
supposed to grow. So giving it to them won't make them a 7'0 Center for
| | | | | | | | | | | | | |
UK.
|
Nursing considerations for Growth Hormone therapy - CORRECT
| | | | | | | |
ANSWER✔✔-serial blood draws q 30 minutes for 3-hours following | | | | | | | | |
stimulation with insulin or glycogen. | | | |
Treat with chronological age not developmental age
| | | | | |
Incomplete puberty - CORRECT ANSWER✔✔-Premature thelarche
| | | | |
Premature pubarche |
What is considered True or complete precocious puberty - CORRECT
| | | | | | | | | |
ANSWER✔✔-When Puberty HAPPENS EARLY!!! | | |
What drug is for Precocious puberty - CORRECT ANSWER✔✔-Lupron.
| | | | | | | | |
Slows prepubertal growth to normal rates
| | | | |
Given IM monthly
| |
When to Stop Lupron Treatment - CORRECT ANSWER✔✔-Treatment is
| | | | | | | | |
discontinued at age for normal pubertal changes to resume
| | | | | | | |
, Precocious Puberty - CORRECT ANSWER✔✔-a condition in which
| | | | | | | |
puberty begins before the age of 8 in girls and 9 in boys. Testicular
| | | | | | | | | | | | | |
enlargement in boys and breast enlargement in girls 1st sign
| | | | | | | | |
What drug is used for Treatment of CAH - CORRECT ANSWER✔✔-
| | | | | | | | | |
Cortisone to suppress abnormally high secretion of ACTH for LIFE.
| | | | | | | | | |
Reconstructive surgery as required. | | |
What is something a person with CAH should always be wearing? -
| | | | | | | | | | | |
CORRECT ANSWER✔✔-Medical alert Bracelet
| | |
Detection of CAH in males - CORRECT ANSWER✔✔-precocious genital
| | | | | | | | |
development
Detection of CAH in females - CORRECT ANSWER✔✔--Enlarged clitoris
| | | | | | | | |
appears as a small phallus
| | | |
-Fused labia produce saclike structure without testes
| | | | | |
-Internal female sexual organs are intact
| | | | |
Diagnostic Evaluation for CAH - CORRECT ANSWER✔✔--
| | | | | |
Ultrasonography to visualize pelvic organs | | | |
-Chromosome typing for positive sex determination and to rule out any
| | | | | | | | | | |
other genetic anomalies
| |
Questions With Correct Answers
PKU diet to follow - CORRECT ANSWER✔✔-Breast Feeding or PA+ Free
| | | | | | | | | | |
Formula. Restricted PA + Intake Throughout Life; No meat, limited fruits
| | | | | | | | | | |
& vegetables, limited grains
| | |
What happens if people with PKU don't follow their diet - CORRECT
| | | | | | | | | | | |
ANSWER✔✔-Short Attention Span | |
Poor short term memory
| | |
Visual perception problems
| |
Poor motor coordination
| | |
Mood disorders |
Brain structural changes (reduced grey matter)
| | | | |
Safe PKU level - CORRECT ANSWER✔✔-2-6mg/dl
| | | | |
PKU nursing Considerations - CORRECT ANSWER✔✔-Assist with testing
| | | | | | |
Teach parents about diet and need for follow up blood levels
| | | | | | | | | | |
throughout life |
Child may have trouble adhering to diet as ages
| | | | | | | |
,Provide emotional support | |
Genetic counseling |
What kind of diet should a child with Galactosemia Follow - CORRECT
| | | | | | | | | | | |
ANSWER✔✔-lactose free diet; soy formula | | | |
Calcium supplementation. | |
Dark green leafy green veggies are good
| | | | | |
Can galactosemia breastfeed? - CORRECT ANSWER✔✔-NO!!! AVOID!!!
| | | | | | |
Need soy formula and calcium supplementation
| | | | |
Long-term consequences if diet not followed for galactosemia -
| | | | | | | | |
CORRECT ANSWER✔✔-learning disabilities, lower IQs, short attention
| | | | | | |
span, behavior problems
| |
Clinical Manifestations of galactosemia - CORRECT ANSWER✔✔-
| | | | | |
vomiting, weight loss, jaundice (hepatomegaly), lethargy, hypotonia,
| | | | | | |
cataracts (galactose accumulation)
| |
When should growth hormone be given? - CORRECT ANSWER✔✔-
| | | | | | | |
NIGHT TIME!!! Sub Q injections given @ night 5x a week. Is stopped
| | | | | | | | | | | | |
once when child is where they are supposed to be height wise.
| | | | | | | | | | |
,Realistic expectations for Growth hormone - CORRECT ANSWER✔✔-
| | | | | | |
Growth hormone will only make them grow to what they were
| | | | | | | | | | |
supposed to grow. So giving it to them won't make them a 7'0 Center for
| | | | | | | | | | | | | |
UK.
|
Nursing considerations for Growth Hormone therapy - CORRECT
| | | | | | | |
ANSWER✔✔-serial blood draws q 30 minutes for 3-hours following | | | | | | | | |
stimulation with insulin or glycogen. | | | |
Treat with chronological age not developmental age
| | | | | |
Incomplete puberty - CORRECT ANSWER✔✔-Premature thelarche
| | | | |
Premature pubarche |
What is considered True or complete precocious puberty - CORRECT
| | | | | | | | | |
ANSWER✔✔-When Puberty HAPPENS EARLY!!! | | |
What drug is for Precocious puberty - CORRECT ANSWER✔✔-Lupron.
| | | | | | | | |
Slows prepubertal growth to normal rates
| | | | |
Given IM monthly
| |
When to Stop Lupron Treatment - CORRECT ANSWER✔✔-Treatment is
| | | | | | | | |
discontinued at age for normal pubertal changes to resume
| | | | | | | |
, Precocious Puberty - CORRECT ANSWER✔✔-a condition in which
| | | | | | | |
puberty begins before the age of 8 in girls and 9 in boys. Testicular
| | | | | | | | | | | | | |
enlargement in boys and breast enlargement in girls 1st sign
| | | | | | | | |
What drug is used for Treatment of CAH - CORRECT ANSWER✔✔-
| | | | | | | | | |
Cortisone to suppress abnormally high secretion of ACTH for LIFE.
| | | | | | | | | |
Reconstructive surgery as required. | | |
What is something a person with CAH should always be wearing? -
| | | | | | | | | | | |
CORRECT ANSWER✔✔-Medical alert Bracelet
| | |
Detection of CAH in males - CORRECT ANSWER✔✔-precocious genital
| | | | | | | | |
development
Detection of CAH in females - CORRECT ANSWER✔✔--Enlarged clitoris
| | | | | | | | |
appears as a small phallus
| | | |
-Fused labia produce saclike structure without testes
| | | | | |
-Internal female sexual organs are intact
| | | | |
Diagnostic Evaluation for CAH - CORRECT ANSWER✔✔--
| | | | | |
Ultrasonography to visualize pelvic organs | | | |
-Chromosome typing for positive sex determination and to rule out any
| | | | | | | | | | |
other genetic anomalies
| |
