SPAUD 520: Week 6 - Mixed Dysarthria &
AOS questions with complete solutions
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Mixed dysarthria
Heterogeneous group
Occurs when neurologic damage extends into two or more parts of motor system
Characterized by combination of characteristics in single (pure) dysarthria
Neurologic damage crossing anatomical boundaries
Mixed dysarthria: Neurologic Basis
Neurologic damage crossing anatomical boundaries
Any combination of pure dysarthrias
Prominence of each pure dysarthria within mixed dysarthria varies significantly among
individuals
Mixed dysarthria: Etiologies
Degenerative (motor neuron disease, ALS, Friedrich's Ataxia, multiple system atrophy)
Chronic traumatic encephaolopathy
Vascular disorders (Strokes)
Toxic-Metabolic conditions (WIlson's disease)
Demyelinating disordes (Multiple Sclerosis)
,TBI
Motor Neuron Disease (MND)
Collective deficit; ALS
Amyotrophic Lateral Sclerosis (ALS)
Progressive degeneration of any of four areas of motor neurons
Often progresses from affecting two motor neuron groups to all four
-Spinal nerves where they join the spinal cord = flaccid
-Cranial nerves where they join the brainstem = speech
-UMN: corticobulbar & corticospinal tract = spastic
UMN & LMN signs in the limbs or bulbar muscles or both
Diagnosis: clinical profile & testing
Type of mixed dysarthria: mixed flaccid-spastic
, Clinical features: Fatigue, Cramping, Fasciculations, Muscle atrophy, Spasticity, Cognitive deficits
Speech: Imprecise consonants, Hypernasality, Harshness, Slow rate, Monopitch, Short phrases,
Distorted vowels, Excess & equal stress, Strained-strangled voice, “wet” or “gurgly” voice quality
Differential Diagnosis: Progressive muscular atrophy/Spinal muscle atrophy, Progressive bulbar
palsy, Primary Lateral Sclerosis, PLS
Friedrich's Ataxia
Causes neuron degeneration in cerebellum, brainstem, and spinal cord
Inherited degenerative disease
Mixed dysarthria: mixed ataxic-spastic
Speech: Harshness, Breathiness, strained-stangled voice quality, Audible inspiration, Monopitch,
Imprecise consonants & distorted vowels, Abnormal rate, Excess & equal stress
Multiple systems atrophy
Neurodegenerative condition
Collective term for group of degenerative disorders, many including parkinsonian symptoms
AOS questions with complete solutions
A+ rated
Mixed dysarthria
Heterogeneous group
Occurs when neurologic damage extends into two or more parts of motor system
Characterized by combination of characteristics in single (pure) dysarthria
Neurologic damage crossing anatomical boundaries
Mixed dysarthria: Neurologic Basis
Neurologic damage crossing anatomical boundaries
Any combination of pure dysarthrias
Prominence of each pure dysarthria within mixed dysarthria varies significantly among
individuals
Mixed dysarthria: Etiologies
Degenerative (motor neuron disease, ALS, Friedrich's Ataxia, multiple system atrophy)
Chronic traumatic encephaolopathy
Vascular disorders (Strokes)
Toxic-Metabolic conditions (WIlson's disease)
Demyelinating disordes (Multiple Sclerosis)
,TBI
Motor Neuron Disease (MND)
Collective deficit; ALS
Amyotrophic Lateral Sclerosis (ALS)
Progressive degeneration of any of four areas of motor neurons
Often progresses from affecting two motor neuron groups to all four
-Spinal nerves where they join the spinal cord = flaccid
-Cranial nerves where they join the brainstem = speech
-UMN: corticobulbar & corticospinal tract = spastic
UMN & LMN signs in the limbs or bulbar muscles or both
Diagnosis: clinical profile & testing
Type of mixed dysarthria: mixed flaccid-spastic
, Clinical features: Fatigue, Cramping, Fasciculations, Muscle atrophy, Spasticity, Cognitive deficits
Speech: Imprecise consonants, Hypernasality, Harshness, Slow rate, Monopitch, Short phrases,
Distorted vowels, Excess & equal stress, Strained-strangled voice, “wet” or “gurgly” voice quality
Differential Diagnosis: Progressive muscular atrophy/Spinal muscle atrophy, Progressive bulbar
palsy, Primary Lateral Sclerosis, PLS
Friedrich's Ataxia
Causes neuron degeneration in cerebellum, brainstem, and spinal cord
Inherited degenerative disease
Mixed dysarthria: mixed ataxic-spastic
Speech: Harshness, Breathiness, strained-stangled voice quality, Audible inspiration, Monopitch,
Imprecise consonants & distorted vowels, Abnormal rate, Excess & equal stress
Multiple systems atrophy
Neurodegenerative condition
Collective term for group of degenerative disorders, many including parkinsonian symptoms