With Complete Solutions
Cysteine is a nonessential amino acid as it can be synthesized
from: correct answer: Methionine
All transaminiation reactions require: correct answer: Pyridoxal
Phosphate
Synthesis of Tyrosine requires: correct answer:
Tetrahydrobiopterin (BH4)
PKU results from a heritable defect in: correct answer:
Phenylalanine hydroxylase
Phenylkentonuria can also present as a result of a deficiency in:
correct answer: Tetrahydrobiopterin (BH4)
Metabolism of Glycine requires: correct answer:
Tetrhydrofolate
Amino acids are said to be ketogenic if they are metabolized to:
correct answer: Acetyl CoA
The enzyme responsible for freeing ammonia from glutamine to
generate glutamate is: correct answer: Glutaminase
Metabolism of branched chain amino acids such as valine is
particularly high in: correct answer: Skeletal Muscle
, A deficiency in cobalamin would negatively impact which
pathways: correct answer: Transsulfuration of homocysteine &
Remethylation of homocysteine
Which amino acid is exclusively ketogenic? correct answer:
Leusine
In the case of an individual who is autosomal recessive for a
deficiency in cystathione - beta- synthase. Which amino acid
becomes essential? correct answer: Cysteine
Transamination is the first step in amino acid metabolism and it
involves: correct answer: The transfer of an amine group from
an amino acid to a keto acid.
Deficiency in Tyrosine can impact the generation of both
melanin and... correct answer: Dopamine
Hemoglobin bound to heme is termed: correct answer:
Holoprotein
Hemoglobin binds oxygen with a greater affinity in the: correct
answer: R State
Alpha helices and beta sheets are primarily stabilized by: correct
answer: Hydrogen bonding
Aspartate is classified as a(n): correct answer: Charged amino
acid