PEDIATRIC CCRN EXAM SCRIPT 2026
QUESTIONS WITH FULL CORRECT ANSWERS
◉ Define Neurogenic Shoick Answer: Vascular muscle tone
controlled by sympathetic vasomotor system is lost, and extreme
vasodilation occurs
◉ Most common cause of sudden cardiac death in young healthy
athletes Answer: hypertrophic cardiomyopathy
◉ Describe Hypertrophic Cardiomyopathy Answer: Thickening of
the LV and mostly septum without dilation. Mitral valve regurg.
occurs and atypical filling pressure and LV outflow tract obstruction
◉ What is the most common sign of Hypertrophic Cardiomyopathy?
Answer: Syncope due to arrhythmias
◉ What are manifestations of Hypertrophic Cardiomyopathy?
Answer: Dyspnea
angina (especially with exertion)
palpitations
murmurs
dysrhythmias
,◉ Name the 3 most common ways to manage Hypertrophic
Cardiomyopathy Answer: 1. Beta Blockers: decreases HR to prolong
diastole and relaxation
2. Calcium channel blockers: ventricular relaxation
3. Septal myectomy
◉ Describe Dilated Cardiomyopathy Answer: Dilated Ventricle leads
to thinner muscular wall, which inhibits the ventricle from
contracting normally and as forcefully. Myocardial stretch increases
(think floppy ventricle), so this heart enlarges to compensate and
deliver more blood with each beat
◉ What is the least common type of cardiomyopathy? Answer:
Restrictive
◉ Describe Restrictive Cardiomyopathy Answer: Ventricle walls
stiffen and prevent the heart from properly filling with blood, which
leads to minimal contractile movement of blood
◉ What will a chest XR, EKG, ECHO, and cath help to diagnose
Answer: CXR-enlargement
EKG-Conduction issues
ECHO- contractility
,Cath- cardiac fxn and biopsy
◉ What are the differences in treatment plans for Hypertrophic vs.
Dilated Cardiomyopathy? Answer: Hypertrophic treatment is careful
with the use of inotropes while inotropes and digoxin are used in
dilated treatment to improve contractility Beta agonist and Ca
channel blockers are used in hypertrophic to decrease afterload and
contractility while beta blockers are used in dilated to counter the
sympathetic stim.
◉ What are surgical interventions for Cardiomyopathy? Answer: -
Septal myotomy
-pacing
-transplant
-Fluid and sodium restriction
◉ What is Long QT Syndrome caused by? Answer: Defect in ion
channels of cardiac cells causing abnormal ventricular
repolarization, prolonged QT interval, and abnormal T wave
◉ What are triggers for Long QT syndrome? Answer: Exercise
◉ What is the most common risk factor of Long QT syndrome?
Answer: Risk for torsades de pointes
, ◉ How can Long QT syndrome be managed? Answer: -ICD
-Denervation surgery
-Potassium rich diet
-Beta blockers
-sodium channel blockers
-omega 3 fatty acid supps
◉ What is the number 1 birth defect? Answer: Congenital Heart
diseases
◉ What is the leading cause of death in infancy from a birth defect?
Answer: Congenital Heart disease
◉ Name risk factors for Congenital Heart Disease Answer: Maternal
Age
Trisomy 21
alcohol ingestion
anti-convulsant ingestion
diabetes
rubella in pregnancy
coxsackie virus exposure
QUESTIONS WITH FULL CORRECT ANSWERS
◉ Define Neurogenic Shoick Answer: Vascular muscle tone
controlled by sympathetic vasomotor system is lost, and extreme
vasodilation occurs
◉ Most common cause of sudden cardiac death in young healthy
athletes Answer: hypertrophic cardiomyopathy
◉ Describe Hypertrophic Cardiomyopathy Answer: Thickening of
the LV and mostly septum without dilation. Mitral valve regurg.
occurs and atypical filling pressure and LV outflow tract obstruction
◉ What is the most common sign of Hypertrophic Cardiomyopathy?
Answer: Syncope due to arrhythmias
◉ What are manifestations of Hypertrophic Cardiomyopathy?
Answer: Dyspnea
angina (especially with exertion)
palpitations
murmurs
dysrhythmias
,◉ Name the 3 most common ways to manage Hypertrophic
Cardiomyopathy Answer: 1. Beta Blockers: decreases HR to prolong
diastole and relaxation
2. Calcium channel blockers: ventricular relaxation
3. Septal myectomy
◉ Describe Dilated Cardiomyopathy Answer: Dilated Ventricle leads
to thinner muscular wall, which inhibits the ventricle from
contracting normally and as forcefully. Myocardial stretch increases
(think floppy ventricle), so this heart enlarges to compensate and
deliver more blood with each beat
◉ What is the least common type of cardiomyopathy? Answer:
Restrictive
◉ Describe Restrictive Cardiomyopathy Answer: Ventricle walls
stiffen and prevent the heart from properly filling with blood, which
leads to minimal contractile movement of blood
◉ What will a chest XR, EKG, ECHO, and cath help to diagnose
Answer: CXR-enlargement
EKG-Conduction issues
ECHO- contractility
,Cath- cardiac fxn and biopsy
◉ What are the differences in treatment plans for Hypertrophic vs.
Dilated Cardiomyopathy? Answer: Hypertrophic treatment is careful
with the use of inotropes while inotropes and digoxin are used in
dilated treatment to improve contractility Beta agonist and Ca
channel blockers are used in hypertrophic to decrease afterload and
contractility while beta blockers are used in dilated to counter the
sympathetic stim.
◉ What are surgical interventions for Cardiomyopathy? Answer: -
Septal myotomy
-pacing
-transplant
-Fluid and sodium restriction
◉ What is Long QT Syndrome caused by? Answer: Defect in ion
channels of cardiac cells causing abnormal ventricular
repolarization, prolonged QT interval, and abnormal T wave
◉ What are triggers for Long QT syndrome? Answer: Exercise
◉ What is the most common risk factor of Long QT syndrome?
Answer: Risk for torsades de pointes
, ◉ How can Long QT syndrome be managed? Answer: -ICD
-Denervation surgery
-Potassium rich diet
-Beta blockers
-sodium channel blockers
-omega 3 fatty acid supps
◉ What is the number 1 birth defect? Answer: Congenital Heart
diseases
◉ What is the leading cause of death in infancy from a birth defect?
Answer: Congenital Heart disease
◉ Name risk factors for Congenital Heart Disease Answer: Maternal
Age
Trisomy 21
alcohol ingestion
anti-convulsant ingestion
diabetes
rubella in pregnancy
coxsackie virus exposure
