Cystic Fibrosis Study Guide Exam And
All Actual Answers.
During the advanced stages of cystic fibrosis, the anatomic alterations cause the patient to have: -
Answer A primarily obstructive lung disease
When the CFTR gene becomes dysfunctional, there are abnormal transportation of what electrolyte(s)? -
Answer Chloride and Sodium
Your patient has a lung infection with Pseudomonas Aeruginosa. What antibiotic should be used against
it? - Answer Tombramycin (TOBI)
What complicating pulmonary problem is likely to happen to a patient with cystic fibrosis? - Answer
Spontaneous pneumothorax
Over 1000 different mutations in the gene that encodes for.. - Answer Cystic Fibrosis Transmembrane
Conductance Regulator (CFTR)
Cystic Fibrosis is an autosomal recessive gene disorder caused by mutations in a pair of genes located
on.. - Answer Chromosome 7
Common chest assessment findings in a patient with cystic fibrosis include: - Answer -Hyperresonant
percussion note
-Diminished breath sounds
-Crackles, rhonchi, and wheezing
What test is a reliable test for the identification of approximately 98% of patients with Cystic Fibrosis? -
Answer Sweat Test (measures amount of chloride and sodium in pts sweat)
Major pathologic or structural changes associated with CF are: - Answer -Excessive production and
accumulation of thick, tenacious mucous in the tracheobronchial tree
All Actual Answers.
During the advanced stages of cystic fibrosis, the anatomic alterations cause the patient to have: -
Answer A primarily obstructive lung disease
When the CFTR gene becomes dysfunctional, there are abnormal transportation of what electrolyte(s)? -
Answer Chloride and Sodium
Your patient has a lung infection with Pseudomonas Aeruginosa. What antibiotic should be used against
it? - Answer Tombramycin (TOBI)
What complicating pulmonary problem is likely to happen to a patient with cystic fibrosis? - Answer
Spontaneous pneumothorax
Over 1000 different mutations in the gene that encodes for.. - Answer Cystic Fibrosis Transmembrane
Conductance Regulator (CFTR)
Cystic Fibrosis is an autosomal recessive gene disorder caused by mutations in a pair of genes located
on.. - Answer Chromosome 7
Common chest assessment findings in a patient with cystic fibrosis include: - Answer -Hyperresonant
percussion note
-Diminished breath sounds
-Crackles, rhonchi, and wheezing
What test is a reliable test for the identification of approximately 98% of patients with Cystic Fibrosis? -
Answer Sweat Test (measures amount of chloride and sodium in pts sweat)
Major pathologic or structural changes associated with CF are: - Answer -Excessive production and
accumulation of thick, tenacious mucous in the tracheobronchial tree
