RNC NIC 2026 PRETERM INFANT CARE AND
DEVELOPMENTAL SUPPORT ASSESSMENT
PAPER VERIFIED SUMMARY
◉ Most common CHD with Trisomy 21
Answer: Endocardial cushion defect
◉ Obstructive CHD's with pulmonary venous congestion
Answer: 1) coarctation of aorta
2) aortic stenosis
◉ Most common CHD associated with Turner's syndrome
Answer: Coarctation of aorta
◉ Treatment of coarctation of aorta
Answer: Treat CHF aggressively
PGE1 to maintain DA
Surgical repair (can reoccur)
◉ Aortic stenosis signs/symptoms
Answer: None at birth
,Grade 2-6 harsh systolic murmur in upper RSB
CHF S/S delayed by weeks but progresses rapidly
◉ Aortic stenosis treatment
Answer: If critical PGE to maintain DA.
First, balloon valvuloplasty (usually successful)
Surgery if fails
◉ Obstructive defects with decreased pulmonary blood flow
Answer: 1) TOF
2) pulmonary stenosis
3) pulmonary atresia
4) tricuspid atresia
◉ Most common cyanotic heart lesion
Answer: TOF
◉ TOF on chest x-ray
Answer: Boot shaped heart, normal size
◉ Components of TOF
Answer: 1) pulmonary stenosis
,2) VSD
3) aorta overrides VSD
4) RV hypertrophy
◉ Mixed CHD
Answer: 1) TGV
2) Truncus arteriosus
3) TAPVR
4) HLHS
◉ Truncus arteriosus associated with which syndrome
Answer: Di George Syndrome
◉ CXR heart has appearance of "egg on a string"
Answer: TGV
◉ 4 pulmonary veins attached to the venous system, returning
oxygenated blood to the right side of the heart instead of left atrium
Answer: TAPVR
◉ TAPVR
Answer: Need patent foramen ovale or true ASD for survival
, ◉ Most common cardiac cause of death in the first week of life
Answer: Hypoplastic left heart syndrome
◉ Presentation of hypoplastic left heart syndrome
Answer: Asymptomatic at birth with rapid deterioration as PDA
closes
◉ Hypoplastic left heart syndrome treatment
Answer: PGE1
Afterload decreasing agents
Aggressive management of acidosis
Transcatheter balloon atrial septostomy to decompress LA
Staged surgical repair or transplant
◉ PGE1 dosing
Answer: 0.05-0.1 mcg/kg/min
Side effects-apnea, hypotension
◉ Consistent finding that reflects RV volume overload
Answer: Hyperdynamic precordial activity
DEVELOPMENTAL SUPPORT ASSESSMENT
PAPER VERIFIED SUMMARY
◉ Most common CHD with Trisomy 21
Answer: Endocardial cushion defect
◉ Obstructive CHD's with pulmonary venous congestion
Answer: 1) coarctation of aorta
2) aortic stenosis
◉ Most common CHD associated with Turner's syndrome
Answer: Coarctation of aorta
◉ Treatment of coarctation of aorta
Answer: Treat CHF aggressively
PGE1 to maintain DA
Surgical repair (can reoccur)
◉ Aortic stenosis signs/symptoms
Answer: None at birth
,Grade 2-6 harsh systolic murmur in upper RSB
CHF S/S delayed by weeks but progresses rapidly
◉ Aortic stenosis treatment
Answer: If critical PGE to maintain DA.
First, balloon valvuloplasty (usually successful)
Surgery if fails
◉ Obstructive defects with decreased pulmonary blood flow
Answer: 1) TOF
2) pulmonary stenosis
3) pulmonary atresia
4) tricuspid atresia
◉ Most common cyanotic heart lesion
Answer: TOF
◉ TOF on chest x-ray
Answer: Boot shaped heart, normal size
◉ Components of TOF
Answer: 1) pulmonary stenosis
,2) VSD
3) aorta overrides VSD
4) RV hypertrophy
◉ Mixed CHD
Answer: 1) TGV
2) Truncus arteriosus
3) TAPVR
4) HLHS
◉ Truncus arteriosus associated with which syndrome
Answer: Di George Syndrome
◉ CXR heart has appearance of "egg on a string"
Answer: TGV
◉ 4 pulmonary veins attached to the venous system, returning
oxygenated blood to the right side of the heart instead of left atrium
Answer: TAPVR
◉ TAPVR
Answer: Need patent foramen ovale or true ASD for survival
, ◉ Most common cardiac cause of death in the first week of life
Answer: Hypoplastic left heart syndrome
◉ Presentation of hypoplastic left heart syndrome
Answer: Asymptomatic at birth with rapid deterioration as PDA
closes
◉ Hypoplastic left heart syndrome treatment
Answer: PGE1
Afterload decreasing agents
Aggressive management of acidosis
Transcatheter balloon atrial septostomy to decompress LA
Staged surgical repair or transplant
◉ PGE1 dosing
Answer: 0.05-0.1 mcg/kg/min
Side effects-apnea, hypotension
◉ Consistent finding that reflects RV volume overload
Answer: Hyperdynamic precordial activity
