CPHON EXAM REVIEW; QUESTIONS
WITH DETAILED VERIFIED ANSWERS;
ALREADY GRADED A; 2026
6 nursing assessment and interventions for AIHA - correct
answer- 1. Read labs for decreased hemoglobin 2. Monitor for
anemia 3. Monitor for transfusion complications (rxn and fluid
overload) 4. Maximize child's physical tolerance 5. Teach family
about AIHA 6. Teach aout post slenectomy care prn
Acute Chest is treated with: (4) - correct answer- 1. abx 2.
pain management 3. increased oxygenation 4. transfusions (RBC
or exchange) Rare- mechanical ventilation
Acute Complications of SCD are: (6) - correct answer- 1.
Fever and infection 2. Pain Crisis 3. Acute Chest Syndrome 4.
Splenic Sequestration 5. Aplastic Crisis 6. Cerebral Vascular
Accident of Stroke
Acute nursing goals for pt with SCD crisis: - - correct answer-
Assess - PE - Review Labs - ABX with fever -aggressive hydration -
pain management - pRBC as indictated - cultures - chest xray
,Alpha thalassemia : - - correct answer- two gene
abnormality or greater - mild microcytic and hypochromic
anema c 3 gene deletions = Hemoglobin H - moderate to severe
c 4 gene deletions = Hydrops Fetalis - not compatible with
postnatal life
Aplastic Crisis is most common associated with what virus in
SCD? - correct answer- parvo B19 infection ( usually fifth
disease)
Autoimmune Hemolytic Anemia is a group of disorders
characterized by - correct answer- malfunction of the
immune system where antibodies are produced against antigens
on the surface of RBSs, resulting in hemolysis
Average life span of person with SCD: - correct answer- 45-
65 years
Bone Marrow Failure happens as a results of (3) - correct
answer- 1. deceas or damage to stem cells and their
microenviroment ( hypoplatic or aplastic) 2. matruation defects (
deficiency of Vit B 12 or folate) 3. differentation defects, such as
myelodysplasia
, Causes of AIHA (4) - correct answer- 1. Autoimmune
disorders (LUPUS) 2. Infections (hepatitis, EBV, myco pneu) 3.
Drugs (peni and quinine) 4. Hematologic disorders(Evan's
syndrome and paroxysmal nocturnal hemoglobinuria)
Chronic burden on the heart of anemia often results in (2): - -
correct answer- cardiomegaly - EKG changes
Chronic Complications with SCD (8) : - correct answer- 1.
Retinopathy 2. Cardiac and pulmonary changes 3. cholelithiasis
4. Avascular necrosis 5. Renal Impairment 6. Leg Ulcers 7.
Delayed Growth and maturation 8. Impaired Cognition
Chronic neutropenia predisposes children to what other
complications (3) ? - - correct answer- oral (gingivitis and
periodontal disease) - Orthopedic ( bone demineralization) - and
a subgroup have incr'd risk for MDS and AML
Classic symptoms of Faconi Anemia: - - - correct answer- skin
pigment changes: darkened area of skin, cafe au lait spots,
vitiligo - short stature - limbs anomalies - small testicles, genital
changes - skeletal anomalies: hip, spine, rib - microcephaly - eye
and eyelid abnormalities - ear abnorm; deafness broadened
nose - kidney malformation: absent or horseshoe or hypoplastic
WITH DETAILED VERIFIED ANSWERS;
ALREADY GRADED A; 2026
6 nursing assessment and interventions for AIHA - correct
answer- 1. Read labs for decreased hemoglobin 2. Monitor for
anemia 3. Monitor for transfusion complications (rxn and fluid
overload) 4. Maximize child's physical tolerance 5. Teach family
about AIHA 6. Teach aout post slenectomy care prn
Acute Chest is treated with: (4) - correct answer- 1. abx 2.
pain management 3. increased oxygenation 4. transfusions (RBC
or exchange) Rare- mechanical ventilation
Acute Complications of SCD are: (6) - correct answer- 1.
Fever and infection 2. Pain Crisis 3. Acute Chest Syndrome 4.
Splenic Sequestration 5. Aplastic Crisis 6. Cerebral Vascular
Accident of Stroke
Acute nursing goals for pt with SCD crisis: - - correct answer-
Assess - PE - Review Labs - ABX with fever -aggressive hydration -
pain management - pRBC as indictated - cultures - chest xray
,Alpha thalassemia : - - correct answer- two gene
abnormality or greater - mild microcytic and hypochromic
anema c 3 gene deletions = Hemoglobin H - moderate to severe
c 4 gene deletions = Hydrops Fetalis - not compatible with
postnatal life
Aplastic Crisis is most common associated with what virus in
SCD? - correct answer- parvo B19 infection ( usually fifth
disease)
Autoimmune Hemolytic Anemia is a group of disorders
characterized by - correct answer- malfunction of the
immune system where antibodies are produced against antigens
on the surface of RBSs, resulting in hemolysis
Average life span of person with SCD: - correct answer- 45-
65 years
Bone Marrow Failure happens as a results of (3) - correct
answer- 1. deceas or damage to stem cells and their
microenviroment ( hypoplatic or aplastic) 2. matruation defects (
deficiency of Vit B 12 or folate) 3. differentation defects, such as
myelodysplasia
, Causes of AIHA (4) - correct answer- 1. Autoimmune
disorders (LUPUS) 2. Infections (hepatitis, EBV, myco pneu) 3.
Drugs (peni and quinine) 4. Hematologic disorders(Evan's
syndrome and paroxysmal nocturnal hemoglobinuria)
Chronic burden on the heart of anemia often results in (2): - -
correct answer- cardiomegaly - EKG changes
Chronic Complications with SCD (8) : - correct answer- 1.
Retinopathy 2. Cardiac and pulmonary changes 3. cholelithiasis
4. Avascular necrosis 5. Renal Impairment 6. Leg Ulcers 7.
Delayed Growth and maturation 8. Impaired Cognition
Chronic neutropenia predisposes children to what other
complications (3) ? - - correct answer- oral (gingivitis and
periodontal disease) - Orthopedic ( bone demineralization) - and
a subgroup have incr'd risk for MDS and AML
Classic symptoms of Faconi Anemia: - - - correct answer- skin
pigment changes: darkened area of skin, cafe au lait spots,
vitiligo - short stature - limbs anomalies - small testicles, genital
changes - skeletal anomalies: hip, spine, rib - microcephaly - eye
and eyelid abnormalities - ear abnorm; deafness broadened
nose - kidney malformation: absent or horseshoe or hypoplastic
