CPHON-HEMATOLOGY QUESTIONS
WITH DETAILED VERIFIED
ANSWERS; ALREADY GRADED A
1972 Sickle Cell Anemia Control Act - correct answer-
Provided funds for screening & counseling, research on
epidemiology & hx of disease, pt education
3 cellular elements of blood plasma - correct answer-
albumin, electrolytes, & proteins (clotting factors, fibrinogen,
antibodies)
3 Factors that increase risk of thromboembolism - correct
answer- Factor V Leiden
Protein C & S deficiency
Protein C & S act as Vitamin K dependent proteins which are
anticoagulants
3 parts of blood - correct answer- red blood cells, white
blood cells, platelets
,80% of hemorrhage occurs in joints of kids who have this
disease. Ankle most common site - correct answer-
Hemophilia A
A 13-month-old infant presents with a continuous nose bleed.
The patient's laboratory values reveal hemoglobin 13g/dL;
absolute neutrophil count 1545/mm3; and platelets 8/mm3.
Which of the following will be the most likely initial treatment?
Intravenous immunoglobulins
Splenectomy
Recombinant human factor VIIa
Platelet transfusion - correct answer- IVIG is preferred over
corticosteroids for treatment of ITP
A child presents with malaise, dizziness, jaundice, dyspnea &
tachycardia. What does the nurse expect the lab results to
reveal?
-Pancreatitis
-Renal toxicity
,-Anemia
-Neutropenia - correct answer- Anemia
-clinical presentation includes:
behavioral changes, skin color changes, dyspnea, & tachycardia
A child with dysmorphic thumbs is newly dx with myelodyplastic
syndrome. What does the RN anticipate an additional evaluation
for? - correct answer- Fanconi Anemia
A patient diagnosed with idiopathic thrombocytopenic purpura
(ITP) asks the nurse if this will affect him for the rest of his life.
What should the nurse tell the patient? - correct answer-
"90% of children recover within 12 months.
A patient presents with malaise, dizziness, jaundice, dyspnea, &
tachycardia. What do you anticipate the lab work to show? -
correct answer- Anemia
A patient with a history of severe hemophilia A & an inhibitor
presents with swollen knee. The nurse anticipates which drug
therapy? - correct answer- Factor VII a
, A patient with irritability, nystagmus, ataxia, lethargy & vomiting
shows symptoms of: - correct answer- Posterior Fossa
syndrome
A rare inherited disorder leading to elevated unconjugated
bilirubin, causing kerinictus, brain damage, death - correct
answer- Crigler-Najjar Syndrome
Acquired autoimmune thrombo, most common in kids 2-6yrs,
with antecedent viral illness, chronic type more in adults, f>m,
plts <50, no hemolysis or schistocytes on smear - correct
answer- Idiopathic Thrombocytopenic Purpura (ITP)
ADH is stored in the - correct answer- pituitary gland
Adopted Chinese girl with a Hgb of 5, diagnosis? - correct
answer- Beta Thal
After removal of pituitary - correct answer- 3 days after
large amounts of ADH are released- leads to no UO, low Na,
weight gain
WITH DETAILED VERIFIED
ANSWERS; ALREADY GRADED A
1972 Sickle Cell Anemia Control Act - correct answer-
Provided funds for screening & counseling, research on
epidemiology & hx of disease, pt education
3 cellular elements of blood plasma - correct answer-
albumin, electrolytes, & proteins (clotting factors, fibrinogen,
antibodies)
3 Factors that increase risk of thromboembolism - correct
answer- Factor V Leiden
Protein C & S deficiency
Protein C & S act as Vitamin K dependent proteins which are
anticoagulants
3 parts of blood - correct answer- red blood cells, white
blood cells, platelets
,80% of hemorrhage occurs in joints of kids who have this
disease. Ankle most common site - correct answer-
Hemophilia A
A 13-month-old infant presents with a continuous nose bleed.
The patient's laboratory values reveal hemoglobin 13g/dL;
absolute neutrophil count 1545/mm3; and platelets 8/mm3.
Which of the following will be the most likely initial treatment?
Intravenous immunoglobulins
Splenectomy
Recombinant human factor VIIa
Platelet transfusion - correct answer- IVIG is preferred over
corticosteroids for treatment of ITP
A child presents with malaise, dizziness, jaundice, dyspnea &
tachycardia. What does the nurse expect the lab results to
reveal?
-Pancreatitis
-Renal toxicity
,-Anemia
-Neutropenia - correct answer- Anemia
-clinical presentation includes:
behavioral changes, skin color changes, dyspnea, & tachycardia
A child with dysmorphic thumbs is newly dx with myelodyplastic
syndrome. What does the RN anticipate an additional evaluation
for? - correct answer- Fanconi Anemia
A patient diagnosed with idiopathic thrombocytopenic purpura
(ITP) asks the nurse if this will affect him for the rest of his life.
What should the nurse tell the patient? - correct answer-
"90% of children recover within 12 months.
A patient presents with malaise, dizziness, jaundice, dyspnea, &
tachycardia. What do you anticipate the lab work to show? -
correct answer- Anemia
A patient with a history of severe hemophilia A & an inhibitor
presents with swollen knee. The nurse anticipates which drug
therapy? - correct answer- Factor VII a
, A patient with irritability, nystagmus, ataxia, lethargy & vomiting
shows symptoms of: - correct answer- Posterior Fossa
syndrome
A rare inherited disorder leading to elevated unconjugated
bilirubin, causing kerinictus, brain damage, death - correct
answer- Crigler-Najjar Syndrome
Acquired autoimmune thrombo, most common in kids 2-6yrs,
with antecedent viral illness, chronic type more in adults, f>m,
plts <50, no hemolysis or schistocytes on smear - correct
answer- Idiopathic Thrombocytopenic Purpura (ITP)
ADH is stored in the - correct answer- pituitary gland
Adopted Chinese girl with a Hgb of 5, diagnosis? - correct
answer- Beta Thal
After removal of pituitary - correct answer- 3 days after
large amounts of ADH are released- leads to no UO, low Na,
weight gain
