ACTUAL Questions and CORRECT
Answers
INTIAL STAGE IN REPAIRING HYPOPLASTIC LEFT HEART SYNDROME - CORRECT
ANSWER - NORWOOD
3 GOALS OF NORWOOD - CORRECT ANSWER - 1. USING THE PA TO INC
AORTIC BLD FLOW
2. ARTERIAL SEPTECTOMY
3. REPAIRING COARCTION VIA BT SHUNT
PURPOSE OF NORWOOD - CORRECT ANSWER - TO KEEP THE PDA OPEN VIA
PGE 1
WHAT IS THE ONLY ALTERNATIVE TO NORWOOD - CORRECT ANSWER -
HEART TRANSPLANT
AT WHAT AGE DO THE RISKS OF HLHS BECOME GREATER IF THE PDA CLOSES? -
CORRECT ANSWER - > 1MO
BLALOCK-TAUSSIG SHUNT - CORRECT ANSWER - BYPASSES THE
OBSTRUCTION OF PULMONARY BLD FLOW TO THE LUNGS BY SUBCLAVIAN-
PULMONARY REDIRECTING
WHEN IS THE B-T SHUNT USED - CORRECT ANSWER - STAGE ONE OF
NORWOOD + CYANOTIC HEART DEFECTS (TET OF FALLOT)
WHAT IS THE PATIENT OXYGEN SATURATION GOAL AFTER B-T SHUNT
PLACEMENT - CORRECT ANSWER - 70-85%
, (ANYTHING HIGHER LEADS TO OVER SHUNTING)
WHAT AND WHEN IS STAGE 2 OF HLHS - CORRECT ANSWER - GLENN SHUNT
B/W 6-9MO
WHAT IS THE PURPOSE OF A GLENN SHUNT - CORRECT ANSWER - TO INC
PULMONARY BLD FLOW BI-DIRECTIONALLY FROM THE SVC TO RIGHT PA
WHEN ARE GLENN SHUNTS NOT USED - CORRECT ANSWER - TET OF FALLOT
ALLOWS 1 VENTRICLE TO PROVIDE BLD FLOW TO THE PULMONARY AND
SYSTEMIC CIRCULATION - CORRECT ANSWER - FONTAN PROCEDURE (STAGE
3 OF HLHS)
BECAUSE PULMONARY BLD FLOW IS DRIVEN BY CVP... - CORRECT ANSWER -
PULMONARY VASCULAR RESISTANCE MUST REMAIN LOW
HOW IS CVP MAINTAINED IN THE FONTAN PROCEDURE? - CORRECT
ANSWER - WITH IVF
(one of the only exceptions in heart kiddos)
4 COMPONENTS OF TETRALOGY OF FALLOT - CORRECT ANSWER - 1. LARGE
VSD
2. RIGHT VENTRICULAR HYPERTROPHY
3. OVERRIDING AORTA
4. PULMONARY STENOSIS
4 KEY S/SX OF TOF - CORRECT ANSWER - 1. CYANOSIS
2. ACTIVITY INTOLERANCE --> TET SPELLS
3. BOOT-SHAPED HEART