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Test Bank For Pediatrics 19th Edition By Nelson 2024.
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, Test Bank For Pediatrics 19th Edition By Nelson 2024.
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WhichfphasefoffKawasakifdiseasefisfassociatedfwithfcoronaryfaneurysms?
A. Acuteffebrilefphase
B. Subacutefphase
C. Convalescentfphase
D. Phasefoffcomplications
E. Allfoffthefabovef-fANSWERf-f1fB.
Kawasakifdiseasefpresentsfwithfcharacteristicallyfhigh,funremittingffeverfandf4foutfoffthef5fpri
ncipalffeatures:
Bilateralfnonexudativefbulbarfconjunctivalfinjectionfwithflimbalfsparing;
Erythemafofftheforalfandfpharyngealfmucosafwithfstrawberryftonguefandfdry,fcrackedflips;fEd
emafandferythemafoffthefhandsfandffeet;
Rashfoffvariousfformsf(scarlatiniform,fmaculopapular,ferythemafmultiforme);fNonsuppur
ativefcervicalflymphadenopathyf(usuallyfunilateral,fwithfnodefsizef>1.5cm).fAcuteffebrilefp
hasef-ffeverfandfthefacutefsignsfoffillnessfandfusuallyflastsf1-2wks
Subacuteffebrilefphasef-
fdesquamation,fthrombocytosis,fcoronaryfaneurysmsfandfhighestfriskfoffsuddenfdeathfusuallyfl
astsf2fwks
Convalescentfphasef-fAllfclinicalfsignsfhavefdisappearedfuntilfESRfnormalizesftypicallyf6-
f 8wksfafterfonsetfonfillness
Source:fNelson'sfTextbookfoffPediatricsf19thfeditionfp864
Affourfyearfoldfpresentsfwithflow-
gradeffever,fintermittentfcrampyfabdominalfpainfwithfemesisfandfswollenfkneesfoff3fdaysfdura
tion.fAfpurpuricfrashfdistributedfbelowfthefkneesfoffbothflowerfextremitiesfisfnotedfonfphysical
fexamination.fThisfpatientfmostflikelyfhas:
A. Meningococcemia
B. Idiopathicfthrombocytopenicfpurpura
C. Henoch-Scholeinfpurpura
D. SLEfE.fJuvenilefRheumatoidfarthritisf-fANSWERf-f2fC.
HSPfisfafcommonfvasculitisfamongfchildrenfandfpresentsfwithfthefclassicffindingsfoffabdomina
lfpainfwithforfwithoutfrectalfbleeding,fvasculitisfrash,farthritisfandfnephritis.fThefplateletfcoun
tfisfnormal.fGastrointestinalfinvolvementfmayfprogressftofintussusception.
Source:fNelson'sfTextbookfoffPediatricsf19thfeditionfp868
Af3fyearfoldffemalefpresentsfwithf1fweekfhistoryfoffdailyf(quotidian)ffeverfassociatedfwithfarth
ritisfoffbothfanklesfandfherfrightfknee.fHerfmotherfnotesfthatfshefhasfdecreasedfactivity
Test Bank For Pediatrics 19th Edition By Nelson 2024.
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, Test Bank For Pediatrics 19th Edition By Nelson 2024.
f f f f f f f f
andfalsofnotesfrashesfthatfcomefandfgofinfdifferentfpartsfoffherfbodyfbutfnotfonfthefface.fOnfphy
sicalfexamination,fsalmonfcoloredfpatchesfwerefnotedfonftheftrunkfandfextremities.fPalpationf
revealedfsplenomegaly.fWhatfisfthefdiagnosis?
A. HenochfSchoenleinfPurpura
B. SystemicfLupusfErythematosus
C. JuvenilefRheumatoidfarthritis
D. JuvenilefDermatomyositis
E. Dengueffeverf-fANSWERf-f3fC.
Don'tfforgetftofstudyfrheumaticfdiseasesfoffchildhoodfevenfiffit'sfnotfyourffavoriteftopic.fFamilia
rizefyourselffwithfthefrelativelyfcommonfonesflikefJRA,fSLEf andfdermatomyositis,f HSPf andf scle
roderma.f Payf attentionf tof thefcharacteristicsf off thef rashf andf otherf features.f(Don'tffallfforfthef
trapfoffrashf+farthritisf=fSLE..fIt'sfnotfalwaysfSLE!)
JRAf-fSalmonfcoloredfpatch,fevanescent,fsparesftheffacefSLEf-
fMalarfrash,fphotosensitive
Dermatomyositisf-
fheliotropef(periorbital)frash,fgottronfpapulesf(rashfonfthefknuckles)fHSPf-
fpurpurafinfdependentfportions
ForfJRA,fknowfthefdifferencesfbetweenfsubtypesf(oligoarticularfvsfpolyarticularfvsfsystemicfons
et)
ThisfcasefinfparticularfisfafcasefoffsystemicfonsetfJuvenilefRheumatoidfarthritisf(alsofcalledfStill'
sfDisease)
Source:fNelson'sfTextbookfoffPediatricsf19thfeditionfp830
Af4fyrfoldfboyfpresentsfwithfhisfthirdfepisodefoffpainfulfcervicalflymphadenitis.fEachfwasftreat
edfwithfincisionfandfdrainagefandfgrewfS.faureus.fHefalsofexperiencesfrecurrentfskinfinfection
s.fAfyearfago,fhefwasfhospitalizedfforfosteomyelitis.fThefmostfimportantflaboratoryftestfis:
A. PCRfforfADAfdeficiency
B. Nitroblueftetrazoliumftest
C. MAC-Ifassay
D. Neutrophilfcount
E. Geneticfchromosomalfanalysisf-fANSWERf-
f4fB.fThisfisfafcasefoffchronicfgranulomatousfdiseasef(CGD)fwhereinfpatientsfarefsusceptibleftof
catalasefpositiveforganismsflikefS.faureus.fThefnitroblueftetrazoliumftestsfthefneutrophilsfabilit
yftofgeneratefsuperoxidefanionfandfthusfkillfingestedfbacteria.
Source:fNelson'sfTextbookfoffPediatricsf19thfeditionfp746
Test Bank For Pediatrics 19th Edition By Nelson 2024.
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, Test Bank For Pediatrics 19th Edition By Nelson 2024.
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WhichfamongftheffollowingfisfnotfafprominentffeaturefoffWiskott-Aldrichfsyndrome?
A. X-linkedfrecessivefinheritance
B. Atopicfdermatitis
C. Thrombocytopenia
D. Recurrentfinfectionsfwithfencapsulatedfbacteria
E. Leukopeniaf-fANSWERf-f5fE.
Note:f Thef prominentf immunologicf impairmentf inf Wiskottf Aldrichf Syndromef isf againstfpol
ysaccharidesfoffencapsulatedforganisms
Source:fNelson'sfTextbookfoffPediatricsf19thfeditionfp734
Af12fyearfoldfseeksfconsultfforf1fdayfhistoryfoffsneezing,fclearfrhinorrheafandfnasalfitchingfnotf
associatedfwithffeverforfanyfotherfsystemicfsymptoms.fPEfrevealsfboggy,fpalefnasalfedemafwit
hfafclearfdischarge.fThefmostflikelyfdiagnosisfis?
A. Foreignfbody
B. Vasomotorfrhinitis
C. Allergicfrhinitis
D. Neutrophilicfrhinitis
E. Rhinitisfmedicamentosaf-fANSWERf-f6fC.
Allergicf rhinitisf isf oftenf seasonalf andf associatedf withf allergicf conjunctivitis.f Eosinophilsfpre
dominatefinfthefnasalfsecretions.fItfisfclassifiedfas:
Seasonalf(cyclical)forfperennialf(allfyear)
Intermittentf (symptomsf occurf <4f daysf perf weekf orf <4f consecutivef weeks)f orf persistentf(sy
mptomsfoccurf>4fdaysfperfweekforf>4fconsecutivefweeks)
Mild-
moderatef(nofimpairment)forfseveref(withfimpairmentfoffdailyfliving/sleep)fSource:fNelso
n'sfTextbookfoffPediatricsf19thfeditionfp775
ThefKasaifprocedurefisfindicatedfforfwhichfofftheffollowing?
A. Neonatalfhepatitis
B. Biliaryfatresia
C. Metabolicfliverfdisease
D. Fulminantfhepaticffailure
E. Nonefoffthefabovef-fANSWERf-f7fB.
DespitefinitialfsuccessfoffthefKasaifoperation,fpatientsfwithfbiliaryfatresiafeventuallyfgetfliverftra
nsplantation.
Source:fNelson'sfTextbookfoffPediatricsf19thfeditionf1387
Test Bank For Pediatrics 19th Edition By Nelson 2024.
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